Cysts arising in the renal corpuscle. A microdissection study.

Congenital hypertension due to unilateral renal vein thrombosis.

“…A boy was born at 34 weeks' of gestation by spontaneous vertex vaginal delivery, 6 days after the onset of acute hydramnios. The membranes had ruptured spontaneously 8 hours before delivery releasing an apparently normal quantity of amniotic fluid.…”

Glomerulocystic Kidneys

“…Taxyand Filmer [ 1], who were the first to discuss GCK, described that glomerular cysts in this disease distributed diffusely in the entire cortex of kidneys but there was neither urinary tract obstruction nor cystic involvement of distal parts of nephron and there were no clinicoanatomical stigmata of a congenital syndrome. However, in the reported cases listed in table 1 [1][2][3][4][5][6][7][8][9][10][11], the kidneys revealed a variety of anatomical conditions and there were various extrarenal anomalies.…”

“…The term GCK was used by Taxyand Filmer [1] in 1976, although Roos [2] documented the first case as polycystic kidney in 1941. This form of renal cystic dis ease is very rare and occurs in infants or young children [1][2][3][4][5][6][7][8][9][10]. Extrarenal anomalies are frequently associated.…”

Glomerulocystic Kidney Disease: A Single Entity?

“…GC can be seen also in adult polycystic kidney disease, kidney dysplasia and obstructive anomalies [9] and genetic disorders [15]. Baxter et al [2] suggested that GCKD is produced late in gestation, by a malformation in nephro genic zone or tubular obstruction. Its pathogenesis remains unknown.…”

“…These cysts are mostly located in the subcapsular area of the renal cortex, while tubular portions of the nephron remain intact. The term GCKD was first used in 1967 to describe an unusual variety of polycystic kidney [1], but both before and since then isolated cases with similar morphological features have been described [2][3][4][5].…”