d-Transposition of Great Arteries and Total Anomalous Pulmonary Venous Connection With Left Ventricular Regression—A Rarity

Samaddar, Avishek; Das, Mrinalendu; Roychowdhury, Saibal; Roy, Mahua; Khan, Wasim Hayat; Sengupta, Ritojyoti; Narayan, Pradeep

doi:10.1177/2150135119878035

Cited by 1 publication

(2 citation statements)

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“…Instead of the pulmonary circulation, the oxygen-rich blood that drains into the RA is delivered to the systemic circulation [21]. Possibly as a result of this reciprocal compensation, cyanosis is less noticeable and may go unrecognized at birth, culminating in an undeveloped and depleted LV as the individual ages [17,18].…”

Section: Presentationmentioning

confidence: 99%

“…A few authors reported surgery as the mainstay of treatment for coexisting TGA and TAPVC. Successful results were obtained using modified atrial switching techniques based on the principles of either Senning [2,6,10,18] or Mustard [5,[7][8][9]17]. However, in recent years, arterial switch operation (ASO) has become the preferred approach for the TGA.…”

Section: Treatmentmentioning

confidence: 99%

See 1 more Smart Citation

Case report of coexisting transposition of the great arteries with supracardiac total anomalous pulmonary venous connection: focus on computed tomography features

Nawawi

Sari

Maryetty

et al. 2023

Egypt J Radiol Nucl Med

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Background The coexisting of transposition of the great arteries (TGA) with total anomalous pulmonary venous connection (TAPVC) is one of the rare anomalies. The incidence of coexisting TAPVC and TGA is unknown with very few cases ever reported. Case presentation We reported a case of a 13-month-old female toddler with history of cyanosis. Echocardiography revealed atrioventricular ambiguity with pulmonary atresia, all PVs drain into the innominate vein via vertical vein (VV), ostium secundum atrial septal defect (ASD) and ventricular septal defect (VSD) were observed. The CT scan confirmed co-occurrence of TGA and TAPVC. All four confluence PVs behind the small left atrium (LA), drains into an ascending lateral large VV, coursing to innominate vein without any PV access into LA. The superior vena cava, right atrium and right ventricle (RV) were dilated. The RV is the origin of the aortic root. The aorta continues on the right side, with an arterial connection to the right pulmonary aberrant artery at the level of the aortic arch. Main pulmonary artery originates from LV and appears atretic with only connection to the left pulmonary artery. Large ASD and VSD were identified. Conclusions TGA and TAPVC are a rare combination and should be suspected in mild-cyanotic cases with levocardia with situs solitus. CT angiography is one of the modalities of choice to characterize the vasculature anomalies.

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Section: Presentationmentioning

confidence: 99%