Deciphering a case of pulmonary hypertension in a young female: Partial anomalous pulmonary venous drainage the culprit

Patel, Hiten; Bhutani, Suchit; Shamoon, Fayez; Virk, Hartaj

doi:10.4103/atm.atm_148_17

Cited by 3 publications

(2 citation statements)

References 11 publications

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“…LA pressure as assessed by PAWP was elevated in 24 patients. In a normal person, each pulmonary vein drains approximately 25% of the total pulmonary blood flow . However, in anomalous pulmonary vein drainage, the shunt flow may be higher as the circulation is preferentially directed to the right side due to lower pressure in the RA and superior vena cava than in the left atrium.…”

Section: Discussionmentioning

confidence: 99%

“…In a normal person, each pulmonary vein drains approximately 25% of the total pulmonary blood flow. 14 However, in anomalous pulmonary vein drainage, the shunt flow may be higher as the circulation is preferentially directed to the right side due to lower pressure in the RA and superior vena cava than in the left atrium. This effect becomes more pronounced in conditions that increase LA pressure such as systemic hypertension or left heart disease.…”

Section: Discussionmentioning

confidence: 99%

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Partial anomalous pulmonary venous drainage in patients presenting with suspected pulmonary hypertension: A series of 90 patients from the ASPIRE registry

et al. 2020

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Background and objective There are limited data regarding patients with PAPVD with suspected and diagnosed PH. Methods Patients with PAPVD presenting to a large PH referral centre during 2007–2017 were identified from the ASPIRE registry. Results Ninety patients with PAPVD were identified; this was newly diagnosed at our unit in 71 patients (78%), despite 69% of these having previously undergone CT. Sixty‐seven percent had a single right superior and 23% a single left superior anomalous vein. Patients with an SV‐ASD had a significantly larger RV area, pulmonary artery and L‐R shunt and a higher % predicted DLCO (all P < 0.05). Sixty‐five patients were diagnosed with PH (defined as mPAP ≥ 25 mm Hg), which was post‐capillary in 24 (37%). No additional causes of PH were identified in 28 patients; 17 of these (26% of those patients with PH) had a PVR > 3 WU. Seven of these patients had isolated PAPVD, five of whom (8% of those patients with PH) had anomalous drainage of a single pulmonary vein. Conclusion Undiagnosed PAPVD with or without ASD may be present in patients with suspected PH; cross‐sectional imaging should therefore be specifically assessed whenever this diagnosis is considered. Radiological and physiological markers of L‐R shunt are higher in patients with an associated SV‐ASD. Although many patients with PAPVD and PH may have other potential causes of PH, a proportion of patients diagnosed with PAH have isolated PAPVD in the absence of other causative conditions.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Partial anomalous pulmonary venous drainage in patients presenting with suspected pulmonary hypertension: A series of 90 patients from the ASPIRE registry

et al. 2020

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Pulmonary Hypertension in COVID-19 Pneumoniae: It Is Not Always as It Seems

Pasqualetto¹,

Sorbo²,

Vitiello³

et al. 2020

European Journal of Case Reports in Internal Medicine

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A patient affected by COVID-19 pneumonia may develop pulmonary hypertension (PH) and secondary right ventricular (RV) involvement, due to lung parenchymal and interstitial damage and altered pulmonary haemodynamics, even in non-advanced phases of the disease. This is a consequence of hypoxic vasoconstriction of the pulmonary circulation, the use of positive end-expiratory pressure (PEEP) in mechanical ventilation, pulmonary endothelial injury, and local inflammatory thrombotic and/or thromboembolic processes. We report the case of a young man admitted with a diagnosis of COVID-19 pneumoniae with PH unrelated to viral infection and in whom partial anomalous pulmonary venous drainage (PAPVD) was eventually diagnosed.

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Types of Correction of the Supracardiac Form of Partial Abnormal Drainage of the Pulmonary Veins. Warden Procedure

Sagatov

Досмаилов

2021

BSK

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The article describes the types of correction of the supracardial form of abnormal drainage of the pulmonary veins. One of the methods of correcting this defect is the Warden operation, which includes: after sternotomy, connection of artificial circulation, cardioplegia, the superior vena cava is cut off, the proximal end is sutured. Next, a right atriotomy is performed, an anastomosis is formed using an autopericardial patch between the abnormal drainage and the left atrium through the ASD. Then an anastomosis is formed between the auricle of the right atrium and the distal end of the superior vena cava. As a result, blood from the abnormal pulmonary veins begins to drain into the left atrium through the ASD.

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Deciphering a case of pulmonary hypertension in a young female: Partial anomalous pulmonary venous drainage the culprit

Cited by 3 publications

References 11 publications

Partial anomalous pulmonary venous drainage in patients presenting with suspected pulmonary hypertension: A series of 90 patients from the ASPIRE registry

Partial anomalous pulmonary venous drainage in patients presenting with suspected pulmonary hypertension: A series of 90 patients from the ASPIRE registry

Pulmonary Hypertension in COVID-19 Pneumoniae: It Is Not Always as It Seems

Types of Correction of the Supracardiac Form of Partial Abnormal Drainage of the Pulmonary Veins. Warden Procedure

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