Delayed Diagnosis and Fate of Congenital Cholesteatoma (Keratoma)

Grundfast, Kenneth M.; Ahuja, Gurpreet S.; Parisier, Simon C.; Culver, Stephanie M.

doi:10.1001/archotol.1995.01890080071014

Cited by 26 publications

(13 citation statements)

References 8 publications

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“…13 Though this condition is congenital, often the diagnosis is delayed because CC may grow for years without causing signs or symptoms and, having grown without early detection. 18 In the present study, all the cases have unilateral ear involvement with right ear more involved. In a study done by Cho et al, all 93 patients had unilateral ear involvement.…”

Section: Methodssupporting

confidence: 47%

Clinical aspects and surgical outcomes of pediatric cholesteatoma in a tertiary care teaching hospital

Gupta

Mirza²,

Gupta

2019

Int J Otorhinolaryngol Head Neck Surg

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Background: Cholesteatoma in children is customarily viewed as a separate and special entity as it presents the otolaryngologist with a verity of diagnostic and therapeutic challenges. The study was planned with objective of studying the clinical aspects and surgical outcomes of pediatric cholesteatoma.Methods: The patients younger than 15 years and diagnosed as congenital cholesteatoma were included in the present study. All the patients underwent thorough clinical examination, laboratory and radiological investigations. Depending on the stage of disease, surgical procedure was decided. All patients were followed-up for at least 12 months after surgery. Results: Total 46 children congenital cholesteatoma (CC) was included in the study. The mean age of diagnosis was 7.08±5.64 years. All the cases have unilateral ear involvement. 14 patients were asymptomatic and CC were found incidental. Patients with CC represented with more commonly with hearing impairment. The CC was most commonly found in the anterosuperior quadrant. All 46 patients with CC underwent operative procedure with transcanal myringotomy was commonest surgical approach. During the 12 month follow-up, 28.86% of patients presented with recurrence of disease.Conclusions:Despite of improved understanding of this disorder with better surgical techniques and skill, high recurrence rate is still major challenge for successful management of CC.

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Section: Methodssupporting

confidence: 47%

Clinical aspects and surgical outcomes of pediatric cholesteatoma in a tertiary care teaching hospital

Gupta

Mirza²,

Gupta

2019

Int J Otorhinolaryngol Head Neck Surg

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“…Rather than being the rarity it was once thought, CC is regularly reported in large series [2][3][4][5][6][7][8][9][10] and, consequently, we have a more accurate understanding of its clinical presentation. The typical patient is a 5-yearold boy with a variable history of otitis media, in whom a white pearly mass behind an intact tympanic membrane is otoscopically observed by a pediatrician or an otolaryngologist.…”

mentioning

confidence: 98%

Congenital Cholesteatoma

Nelson¹,

Roger²,

Koltai³

et al. 2002

Arch Otolaryngol Head Neck Surg

111

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The sequence of spread of CC, involving 3 sites, suggests a natural classification system. The CC usually originates in the anterior superior quadrant, but does not consistently remain there, and may variably occupy the middle ear and mastoid and result in ossicular destruction and conductive hearing loss. The location of CC and the involvement of the ossicles is an accurate predictor of the type of surgery necessary for its control and for the success of hearing restoration.

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“…Roger et al 3 proposed a 4-category system, but it was not exhaustive in that it did not accommodate all possible cases. Grundfast et al 4 described a meticulous reporting system in which presence or absence of disease is noted for each of 12 sites, but no simple staging system was proposed, and few others could reconstruct their findings in such detail from existing records.…”

mentioning

confidence: 99%