Relapsing polychondritis (RP) is a rare, inflammatory, multiorgan disorder affecting cartilaginous structure and other connective tissue. Cardiovascular complications occur in 10%-52% of patients. We report a case of emergency surgery for an acute aortic dissection in a patient with RP. A 45-year-old female who had been taking corticosteroids (10 mg/day) for 2 years for RP presented at another hospital with dyspnea and severe chest and back pain. Acute aortic dissection was diagnosed, and we performed emergency replacement of the ascending aorta. We could not control the bleeding from suture holes of the native aorta because the vessel was so fragile. Thus, we performed a delayed sternal closure. The day after surgery, bleeding had decreased, and we could close the chest wall. Infection was well controlled, and the patient suffered minimal additional complications. She was discharged to home by herself 29 days after surgery and returned to normal life.Keywords: acute aortic dissection, relapsing polychondritis, emergency operation, delayed sternal closure
Case ReportA 45-year-old female presented at the emergency department of another hospital with dyspnea and severe chest and back pain at work. She was diagnosed with acute aortic dissection (Stanford type A) and was transferred to our hospital for emergency surgery. She had a history of RP treated with corticosteroids (10 mg/day) for the previous 2 years. Computed tomography (CT) on admission showed acute aortic dissection (Stanford type A). The dissection started at the right coronary artery and continued to the infrarenal abdominal aorta (Fig. 1). No other medical history was available at the time of admission. We performed emergency surgery. Through a median sternotomy, the dissected, ascending aorta was reconstructed by end-to-end anastomosis with a vascular graft (Triplex Ⓡ 28 mm, Terumo Corporation, Tokyo, Japan) using the less invasive quick replacement (LIQR) technique. 5) Stump plasty was performed with a felt strip sandwiched in the distal and proximal ends. Withdrawal from extracorporeal circulation was uneventful, but bleeding from the needle holes in the native aorta was uncontrollable. As a result of bleeding problem, we could