Dental health and oral health‐related quality of life in children with congenital bleeding disorders

Abstract

Summary. The purpose of this study was to investigate the dental and some other aspects of oral health status of young patients with congenital bleeding disorders (CBD) and the impact of these on their quality of life (OHR-QoL) compared with controls. DMFS-dmfs (Decayed, Missed, Filled Tooth surfaces in permanent and primary teeth) scores, Simplified oral hygiene index, occurance of hypoplasia of first permanent molars, Temporomandibular joint dysfunction and occlusion of 46 CBD patients at the age range of 2-15 years and 46 of other children as control were compared, and the impact of their oral health situation on quality of life was also investigated. Data were analysed by chi-square, t-test and Pearson correlation. Patients were significantly more caries-free with less decayed teeth in primary-permanent dentition (P = 0.03, t = À2.17).The mean scores of OHR-QoL of CBD patients and controls were not significantly different. Oral Bleeding was the significant variable in relation to 'oral health-related quality of life' in CBD groups (Pearson correlation, r = À0.56, P = 0.000). OHR-QoL in the control group was related to dmfs score (r = À0.392, P = 0.011) and male gender (r = À0.329, P = 0.026). Congenital bleeding disorder CBD patients were found to have a better dental health situation in primary dentition compared with controls; however, their 'oral health-related quality of life' was similar. Oral bleeding was the only significant factor related to OHR-QoL in CBD. It shows an overall importance of development of comprehensive care centres for CBD as the main cause of this achievement.

Oral health status in children and adolescents with haemophilia

“…Similar to other studies, majority of these patients attended Specialist Dental Clinics and had regular, scheduled dental appointments [5,18,19]. Similar to other studies, majority of these patients attended Specialist Dental Clinics and had regular, scheduled dental appointments [5,18,19].…”

“…The multidisciplinary approach was also reported in other studies that found similar or lower caries experience among haemophilia patients as compared to healthy controls [5,18,19]. The multidisciplinary approach was also reported in other studies that found similar or lower caries experience among haemophilia patients as compared to healthy controls [5,18,19].…”

Quality of Life in Hemophilia

“…An Iranian study showed that children with a congenital bleeding disorder (aged 2-15 years) have a better dental health situation in primary dentition and a similar oral health-related QoL, assessed with the OHR-QoL, compared to children without congenital bleeding disorders [90].…”

Information provision and attentive listening as determinants of patient perceptions of shared decision-making around chronic illnesses

“…As a result, people with haemophilia can bleed for longer than normal, and some may experience bleeding into joints, muscles, or other parts of their bodies that can lead to joint damage and disability. This disorder, especially in its severe forms, has been associated with mortality and morbidity (Salem and Eshghi 2013). Prophylactic therapy, which involves regular factor replacement (at least three times per week or daily), is of critical importance (Manco-Johnson et al 2007).…”