Dental Management of a Tunisian Child with Sanjad-Sakati Syndrome

Abstract

Sanjad-Sakati syndrome (SSS) is a rare autosomal recessive congenital disorder. The present case report is aimed at describing the orofacial manifestations and dental management of a 4-year seven-month-old, Tunisian boy with SSS. The patient has typical dysmorphic facial features and growth retardation. Intraoral examination revealed micrognathic mandible and maxilla, an arched palate, and small dental arches with an open bite. All the maxillary and mandibular teeth were decayed due to the poor oral hygiene, plaque accumulation, and enamel hypoplasia. Oral rehabilitation involved pulpotomies and root canal therapies on decayed teeth. Resin composite restorations were performed on maxillary and mandibular incisors, and stainless-steel crowns were placed on maxillary and mandibular first and second primary molars. Dental treatment of children with SSS should improve their quality of life and their general health. Undeveloped dental arches associated with dental anomalies as well as learning deficit make very difficult of the oral rehabilitation of such patients.

Knowledge, Attitude, and Behavior of Parents Regarding Early Childhood Caries Prevention of Preschool Children in Western Region of Saudi Arabia: A Cross-Sectional Study

“…Medical conditions or syndromes associated with enamel hypoplasia, physical impairment, decrease in the salivary flow, crowding due to supernumerary teeth, and the presence of cleft lip or palate were also reported as risk factors for ECC [ 5 , 7 ]. Examples of such syndromes are Sanjad–Sakati syndrome (Middle East syndrome), Down syndrome, and Orofaciodigital syndrome [ 7 , 8 , 9 ].…”