Dentin Dysplasia Type I-Diagnosis and Treatment: Case Report

Abstract

This paper aims to report the case of a child with dentin dysplasia type I. An 8 year old female child was referred to the Children's Dental Clinic of the Universidade Federal do Piauí with an aesthetic complaint caused by missing teeth. Four permanent first molars, premolar upper right and upper left permanent canine were present. There was satisfactory oral hygiene and no dental diseases. Anamnesis and laboratory tests did not detect any systemic disorders. Evaluations of initial panoramic radiographs and computed tomography showed permanent teeth with apparently normal crowns, with short and conical roots and obliteration of the pulp chamber, confirming the diagnostic hypothesis of Dentin Dysplasia type I. Root Dentin Dysplasia or Dentin Dysplasia type I is a rare hereditary autosomal dominant disorder, with a complex diagnosis, and the need for evaluation and interdisciplinary planning. There is no specific treatment for this genetic condition. Temporary mucosa-supported prosthesis reimbursed with resilient resin was made to preserve the sites of erupted teeth and those erupting. Monitoring is to be done until the growth of the facial structures is completed, allowing for rehabilitation with fixed prostheses on implants.