Desmoplastic fibroma of the vidian canal in a child: case report

Peridis, S.; Moonim, Mufaddal; Roberts, Deborah H.; Al‐Sarraj, Safa; Hopkins, Claire

doi:10.1017/s002221511100048x

Cited by 7 publications

(3 citation statements)

References 7 publications

(23 reference statements)

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“…[5] reviewed 184 published cases of DF and in a metaanalysis reported the mean age of DF patients at the time of diagnosis as 23 years with a range from 15 months to 75 years. Sex predilection remains unclear while some authors report higher rates of DF in female patients [6] and others report no detectable sex predilection [7]. DF can theoretically affect any bone, but the majority of cases occur in the mandible (22%) and the metaphysis of long bones (56%) [8].…”

Section: Introductionmentioning

confidence: 99%

Desmoplastic Fibroma: A Case Report with Three Years of Clinical and Radiographic Observation and Review of the Literature

Nedopil¹,

Raab²,

Rudert³

2013

TOORTHJ

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Background:Desmoplastic fibroma (DF) is an extremely rare locally aggressive bone tumor with an incidence of 0.11% of all primary bone tumors. The typical clinical presentation is pain and swelling above the affected area. The most common sites of involvement are the mandible and the metaphysis of long bones. Histologically and biologically, desmoplastic fibroma mimics extra-abdominal desmoid tumor of soft tissue.Case Presentation and Literature Review:A case of a 27-year old man with DF in the ilium, including the clinical, radiological and histological findings over a 4-year period is presented here. CT scans performed in 3-year intervals prior to surgical intervention were compared with respect to tumor extension and cortical breakthrough. The patient was treated with curettage and grafting based on anatomical considerations. Follow-up CT scans over 18-months are also documented here. Additionally, a review and analysis of 271 cases including the presented case with particular emphasis on imaging patterns in MRI and CT as well as treatment modalities and outcomes are presented.Conclusion:In patients with desmoplastic fibroma, CT is the preferred imaging technique for both the diagnosis of intraosseus tumor extension and assessment of cortical involvement, whereas MRI is favored for the assessment of extraosseus tumor growth and preoperative planning. While tumor resection remains the preferred treatment for DF, curettage and grafting prove to be an acceptable alternative treatment modality with close follow-up when resection is not possible. Curettage and grafting have been shown to provide good clinical results and are associated with long recurrence free intervals.

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Section: Introductionmentioning

confidence: 99%

Desmoplastic Fibroma: A Case Report with Three Years of Clinical and Radiographic Observation and Review of the Literature

Nedopil¹,

Raab²,

Rudert³

2013

TOORTHJ

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“…Sex predilection remains unclear while some authors report higher rates of desmoplastic fibroma in female patients 5 and others report no detectable sex predilection. 6 Affected patients typically present with a history of a painless, slowly growing mass, often of relatively long duration. 7 Desmoplastic fibroma may involve any bone.…”

Section: Discussionmentioning

confidence: 99%

Rare Case of Infraorbital Desmoplastic Fibroma in a 10-Year-Old: Challenging Diagnosis, Unusual Location and Multidisciplinary Management: A Case Report

Krishna Venkata Rajesh Varma,

Mohapatra,

Jyothy Surendran

et al. 2023

FACE

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Desmoplastic fibroma is a rare benign bone tumor primarily seen in long bones and mandible. Our case was of a 10-year-old with painless infra orbital swelling for which she underwent excision under general anesthesia and reconstruction with orbital plating and iliac crest bone grafting. By its unique clinical presentation and diagnostic challenges encountered in managing this condition, this case report expands our understanding of the disease’s presentation and management, it guides future therapeutic decision-making in similar pediatric cases.

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“…Prior to 2012, only 75 cases of desmoplastic fibroma in the gnathic skeleton have been reported in total [9]. Of note, there has been one reported case of DF afflicting the vidian canal [10].…”

Section: Literature Review and Discussionmentioning

confidence: 99%

Pediatric ethmoid sinus desmoplastic fibroma: Case report and review of pediatric bony sinus tumors

Kadakia

Patel

Iacob

et al. 2015

International Journal of Pediatric Otorhinolaryngology Extra

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Desmoplastic fibroma of the vidian canal in a child: case report

Abstract: Diagnosis and resection of this rare lesion at an earlier stage would have avoided delays in resolving the child's disabling pain. This emphasises the importance of early referral of unusual cases to tertiary centres.

Cited by 7 publications

References 7 publications

Desmoplastic Fibroma: A Case Report with Three Years of Clinical and Radiographic Observation and Review of the Literature

Desmoplastic Fibroma: A Case Report with Three Years of Clinical and Radiographic Observation and Review of the Literature

Rare Case of Infraorbital Desmoplastic Fibroma in a 10-Year-Old: Challenging Diagnosis, Unusual Location and Multidisciplinary Management: A Case Report

Pediatric ethmoid sinus desmoplastic fibroma: Case report and review of pediatric bony sinus tumors

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