Introduction: Sialolithiasis is a disease in which calcified substances accumulate in the ducts or parenchyma of the salivary glands. This disease can occur in people of all ages but is mostly seen in middle-aged adults and rarely in children. This case report aimed to describe a case of sialolithiasis in children Case Report: A 3-year-old girl presented with a lump that enlarged progressively on the right side of the neck since 1 year ago. The patient also complained of painful swallowing. Palpation of the right submandibular revealed a solid, mobile mass measuring 0.5x0.5cm without tenderness or hyperemia. A neck ultrasound showed an enlarged submandibular gland and right parotid gland. A midface and neck multi-slice computed tomography scan (MSCT) supported the diagnosis of sialolithiasis. The patient underwent stone removal with an extraoral approach and general anesthesia. The patient then was discharged with cefixime, methylprednisolone, and paracetamol. Discussion: Sialolithiasis that cannot be removed by opening the canal can be removed by trans-oral or extra-oral sialolithotomy, extracorporeal lithotripsy, sialendoscopy, or laser treatment. Submandibular stones can be removed surgically by intraoral or extraoral approaches. Extraoral approaches are indicated for intra-glandular stones and stones embedded in the hilum of the gland. Conclusion: The diagnosis of sialolithiasis in this patient was confirmed through history taking, physical examination, ultrasound, and a CT scan. Management of sialolithiasis focuses on removing the stone and maintaining salivary gland function. In this case, the stone was removed using an extraoral approach under general anesthesia which resulted in a good outcome