“…Although it was noticeably an atypical finding, mildly dilated proximal MPD in this case was thought to be related to IgG4-associated disease, since it disappeared completely under corticosteroid treatment. High serum levels of IgG4, the presence of type 1 autoimmune pancreatitis (diffuse type) and corticosteroid responsiveness easily helped us to exclude other possible diseases, such as primary sclerosing cholangitis, cholangiocarcinoma, follicular cholangitis, as the differential diagnosis of this case (6,7). Moreover, histological detection of IgG4 + plasma cells is usually unnecessary for cases like ours, showing typical radiological findings and high serum levels of IgG4.…”