Diagnosis and follow‐up of congenital intrahepatic portosystemic venous shunt by ultrasounds

Caiulo, Vito Antonio; Presta, G; Latini, Giuseppe; Mattioli, Girolamo; Vm, Jasonni

doi:10.1111/j.1651-2227.2001.tb03259.x

Cited by 15 publications

(12 citation statements)

References 4 publications

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“…Unlike congenital portocaval shunts, congenital intrahepatic PSS venous shunts can undergo spontaneous closure during the first year of life but the proportion in which this occurs is unknown (Santamaria et al, 1996;Gitzelmann et al, 1997;Ono et al, 1998;Valls et al, 2000;Caiulo et al, 2001). One of the patients in this series (Case 1) demonstrated spontaneous shunt closure in infancy.…”

Section: Intrahepaticmentioning

confidence: 77%

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The clinical anatomy of congenital portosystemic venous shunts

2007

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Congenital portosystemic venous shunts are rare. Their gross anatomy has not been well defined. Four different varieties of congenital portosystemic venous shunts are described in six children seen during a 10-year period, focusing on the anatomy of the shunt as determined by imaging studies and surgery. A detailed review of the literature indicates that congenital portosystemic venous shunts are best classified as: extrahepatic or intrahepatic. Extrahepatic shunts may be further subdivided into portocaval shunts (type 1 end-to-side and type 2 side-to-side) and others. Intrahepatic shunts are due to an abnormal intrahepatic connection between the portal vein and hepatic vein/inferior vena cava or a persistent patent ductus venosus. Additional congenital anomalies, particularly cardiac malformations, may be associated with any type. Some congenital intrahepatic portosystemic venous shunts close spontaneously in infancy; all other congenital portosystemic venous shunts tend to remain patent. To a variable extent, depending largely on the volume and duration of the shunt, affected individuals are at risk of developing hepatic encephalopathy and/or an intrahepatic tumor. The key to understanding the pathogenesis of these shunts lies in the normal developmental mechanisms underlying the formation of the portal vein and inferior vena cava in the embryo.

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Section: Intrahepaticmentioning

confidence: 77%

“…2. A localized peripheral shunt in which one hepatic segment has one or more communications between peripheral branches of the PV and hepatic veins (Valls et al, 2000;Yamagami et al, 2000;Caiulo et al, 2001). 3.…”

Section: Intrahepaticmentioning

confidence: 99%

The clinical anatomy of congenital portosystemic venous shunts

2007

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“…The first two types are the most common 8 , 9 . Our review of past case reports revealed that, in neonatally discovered cases of congenital intrahepatic portosystemic venous shunts, type 2 is the most common, 5 , 10 – 12 followed by type 1, 3 , 6 , 9 , 11 type 3, 2 , 4 , 13 and type 4 12 . In the cases included in this study, all 6 had type 2 lesions, and 1 case among them had 2 type 2 lesions in the medial and lateral segments of the left lobe.…”

Section: Discussionmentioning

confidence: 88%

“…The treatment options for congenital intrahepatic portosystemic venous shunts depend on the shunt ratio and patient's age 17 . The shunts may close spontaneously in most cases by the age of 1 year 2 – 6 , 11 – 13 , 15 or may persist until the age of 2 years 17 . However, treatment by surgery or coil embolization should be performed when the shunt ratio is greater than 60% 17 .…”

Section: Discussionmentioning

confidence: 99%

Congenital Portosystemic Shunts

Han

Park

Song

et al. 2013

Journal of Ultrasound in Medicine

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“…The intrahepatic portal venous shunt in adults is most commonly due to portal venous communication to a systemic vein secondary to portal hypertension. While portosystemic shunts less than 2 mm in diameter are relatively common in patients with cirrhosis, the larger shunts are thought to be congenital [ 2 ]. Popper et al [ 3 ] described many minute communications between the portal and hepatic veins in cirrhotic livers.…”

Section: Discussionmentioning

confidence: 99%

Transhepatic Embolization of Congenital Intrahepatic Portosystemic Venous Shunts with Associated Aneurysms

Paudel

Hoffer

2015

Case Reports in Medicine

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Intrahepatic shunts between the portal and systemic venous systems with associated aneurysms are extremely rare. A middle aged woman presented with hepatic encephalopathy and was found to have two intrahepatic portosystemic venous shunts with associated aneurysms. Diagnosis was made by duplex ultrasound and was confirmed with contrast enhanced MRI. Treatment was performed percutaneously with an Amplatzer vascular plug.

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Diagnosis and follow‐up of congenital intrahepatic portosystemic venous shunt by ultrasounds

Cited by 15 publications

References 4 publications

The clinical anatomy of congenital portosystemic venous shunts

The clinical anatomy of congenital portosystemic venous shunts

Congenital Portosystemic Shunts

Transhepatic Embolization of Congenital Intrahepatic Portosystemic Venous Shunts with Associated Aneurysms

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