Diagnosis and Management of Fontan Failure Secondary to Aortopulmonary Artery Fistula

Abstract

Aortopulmonary artery fistula represents a rare anomalous communication between aorta and pulmonary artery. The treatment of these communications is well established and involves either surgical or percutaneous approach. We present a 15-year-old male with history of hypoplastic left ventricle, hypoplastic aorta and ventricular septal defect with Damus-Kaye-Stansel surgery in the past, who developed acute Fontan circuit failure secondary to the development of aortopulmonary fistula of unknown etiology. Fistula was successfully closed percutaneously, using Amplatzer duct occluder.