Diagnosis of ALCAPA Syndrome in Adults

Alegre-Bayo, Nieves; Algarra-García, José

doi:10.1016/s1885-5857(09)73332-8

Cited by 3 publications

(2 citation statements)

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“…The blood flow restauration in left main coronary artery from the aorta is the primary objective in the surgical correction of ALCAPA, and there are several surgical options in the paediatric population. Derivation of the left subclavian artery and implementation of an aorto-coronary bypass with saphenous vein or the left internal thoracic artery to the left anterior descending coronary have shown low short-term effectiveness (60%) and high morbidity with stenosis and thrombosis of bypass graft 10 – 14 . The Takeuchi procedure is the most used in the paediatric population, however it has a high incidence (> 21%) of supravalvular stenosis of pulmonary artery 15 .…”

Section: Discussionmentioning

confidence: 99%

Case Report: ALCAPA syndrome: successful repair with an anatomical and physiological alternative surgical technique

et al. 2016

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Anomalous left coronary artery from the pulmonary artery, or ALCAPA syndrome, is a rare congenital cardiac disease that can cause myocardial infarction, heart failure and even death in paediatric patients. Only few untreated patients survive until adult age. Here we present the case of a 33-year-old female patient with paroxysmal tachycardia, syncope and mild exertional dyspnoea. She was diagnosed with ALCAPA syndrome and underwent surgical correction with an alternative technique of left main coronary artery extension to the aorta.

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Section: Discussionmentioning

confidence: 99%

Case Report: ALCAPA syndrome: successful repair with an anatomical and physiological alternative surgical technique

et al. 2016

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“…En el abordaje diagnóstico se han utilizado diferentes técnicas para su detección, algunas invasivas, como la arteriografía coronaria 4 , y otras no invasivas, como la TAC de arterias coronarias 5,6 , considerada esta última como de primera línea para el diagnóstico y seguimiento, ya que muestra de manera adecuada la anomalía y tiene el beneficio de aportar información adicional en caso de requerirse manejo quirúrgico 2 . Como parte de los estudios de extensión se han utilizado la RMN de corazón 2 y la perfusión miocárdica 5 para determinar la viabilidad miocárdica y así determinar si los pacientes pueden beneficiarse del tratamiento quirúrgico.…”

Section: B Aunclassified