Diastematomyelia

Abstract

The diagnostic and therapeutic aspects of 10 cases of diastematomyelia are reported. The cutaneous, orthopaedic, neurological, and radiological signs and symptoms are discussed and emphasized. Different embryological and physiopathological aspects are commented on.Surgical treatment is recommended in all cases.

Spinal Dysraphism of a Baby – A Case Report

“…Discussion: Diastematomyelia was initially described as split notochord syndrome (Spina bifida oculta), where developmentally there is longitudinal split of spinal cord. 2,5 Another closely related condition Diplomyelia is encountered with this condition where cord is splitted into two halves from cervical region. 3 In Diastematomyelia cord is duplicated mainly at lumbar region.…”

“…An associated bony, cartilagenous or fibrous spur projecting through the dura mater, forwards from the neural arch, is visible in 33% of cases. 2 Vertebral anomalies (spina bifida, butterfly or hemivertebrae) are common. Laminar fusion associated with a neural arch defect is a good predictor of diastematomyelia and occur at the level of the defect, or at an adjacent level.…”

“…1 Diastematomyelia refers to a type of spinal dysraphism when there is a longitudinal split in the spinal cord. 2 Split cord malformations are a congenital abnormality and account for approximately 4% of all congenital spinal defects. 3 The majority of patients with diastematomyelia are symptomatic, presenting with signs and symptoms of tethered cord, although patients will mild type II variety may be minimally affected or entirely asymptomatic.…”