Differences between the pediatric and adult presentation of fibromuscular dysplasia: results from the US Registry

Green, Rebecca; Gu, Xiaokui; Kline–Rogers, Eva; Froehlich, James B.; Mace, Pamela; Gray, Bruce H.; Katzen, Barry T.; Olin, Jeffrey W.; Gornik, Heather L.; Cahill, A.; Meyers, Kevin

doi:10.1007/s00467-015-3234-z

Cited by 73 publications

(60 citation statements)

References 40 publications

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“…The main cause of renovascular hypertension in this age group is FMD, but in 20-40% of cases renovascular hypertension is a complication of other conditions (syndromic renovascular hypertension), including neurofibromatosis type 1 (> 15%) [65][66][67]. Renovascular hypertension may also be caused by a congenital or acquired (e.g., transplant renal artery stenosis) stenosis of the main renal artery or additional renal arteries and/or segmental branches [68][69].…”

Section: Renovascular Hypertensionmentioning

confidence: 99%

Zalecenia Sekcji Pediatrycznej Polskiego Towarzystwa Nadciśnienia Tętniczego dotyczące postępowania diagnostycznego i terapeutycznego w nadciśnieniu tętniczym u dzieci i młodzieży

Litwin

Niemirska

Obrycki

et al. 2018

Arterial Hypertension

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Presented recommendations are an extended and actualized version of paediatric recommendations of Polish Society of Hypertension published in 2015. Since then, new studies have appeared on this subject, introducing a new classification of hypertension, newly described principles of management in risk groups and methods of assessing hypertensive target organ damage. The presented updated recommendations included changes introduced in the 2016 European Society of Hypertension recommendations and Recommendations of Children's Memorial Health Institute in Warsaw. Recently published guidelines of American Academy of Pediatrics have been discussed. In the presented issue of guidelines, epidemiological information on the occurrence and incidence of hypertension in developmental age was added and classification of blood pressure values was updated. Subchapters on diagnosis and organ damage assessment, principles of diagnosis and treatment of hypertension in children with diabetes, chronic kidney disease and a subsection discussing diagnostic and therapeutic difficulties with setting blood pressure targets were revised. In addition, the principles of early diagnosis of arterial hypertension in post-hospital care in children born before 33 weeks of gestation published in 2018 as recommendations of the Polish Neonatal Society have been also taken into account.

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Section: Renovascular Hypertensionmentioning

confidence: 99%

Zalecenia Sekcji Pediatrycznej Polskiego Towarzystwa Nadciśnienia Tętniczego dotyczące postępowania diagnostycznego i terapeutycznego w nadciśnieniu tętniczym u dzieci i młodzieży

Litwin

Niemirska

Obrycki

et al. 2018

Arterial Hypertension

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“…The French [4][5][6] and the US [7][8][9][10] registries have led to a reappraisal of the frequency, demographic characteristics, classification, pathophysiology, and management of FMD. The face of the disease is evolving from a rare disease of renal arteries accounting for a minority of cases of secondary hypertension in young women to a "systemic" vascular disease affecting renal and also cervico-cephalic, coronary, and iliac arteries 1,11 (Table 1).…”

mentioning

confidence: 99%

Revisiting Fibromuscular Dysplasia

et al. 2016

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“…A 2016 US Registry report found a high prevalence of aneurysm and dissection in the FMD population. Of the 921 patients included in this analysis, 21.6% had an aneurysm and 25.7% had an arterial dissection . Although FMD can affect arteries of any size, involvement of smaller intracranial blood vessels is rare and vertebral FMD without carotid artery involvement is exceptional.…”

Section: Discussionmentioning

confidence: 99%

Hemorrhagic Retinopathy and Optic Nerve Sheath Hemorrhage Associated With Fatal Subarachnoid Hemorrhage from a Ruptured Intracranial Aneurysm Due to Segmental Fibromuscular Dysplasia

Silloca‐Cabana

Hathuc

Harrison

et al. 2019

Journal of Forensic Sciences

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Fibromuscular dysplasia is an idiopathic, nonatheromatous, and noninflammatory arterial disease that most commonly affects the renal and carotid arteries. We report a child with subarachnoid and ocular hemorrhage associated with an aneurysm due to fibromuscular dysplasia. Computed tomography following a witnessed collapse revealed diffuse subarachnoid hemorrhage and severe cerebral edema. An autopsy confirmed the radiographic findings and detected bilateral retinal hemorrhages, optic nerve sheath hemorrhages, and a ruptured saccular aneurysm due to focal fibromuscular dysplasia involving the intracranial right vertebral artery. This case documents a fatal subarachnoid hemorrhage in a child with an intracranial saccular aneurysm caused by fibromuscular dysplasia. The associated retinal hemorrhages are easily detected by postmortem monocular indirect ophthalmoscopy.

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Differences between the pediatric and adult presentation of fibromuscular dysplasia: results from the US Registry

Cited by 73 publications

References 40 publications

Zalecenia Sekcji Pediatrycznej Polskiego Towarzystwa Nadciśnienia Tętniczego dotyczące postępowania diagnostycznego i terapeutycznego w nadciśnieniu tętniczym u dzieci i młodzieży

Zalecenia Sekcji Pediatrycznej Polskiego Towarzystwa Nadciśnienia Tętniczego dotyczące postępowania diagnostycznego i terapeutycznego w nadciśnieniu tętniczym u dzieci i młodzieży

Revisiting Fibromuscular Dysplasia

Hemorrhagic Retinopathy and Optic Nerve Sheath Hemorrhage Associated With Fatal Subarachnoid Hemorrhage from a Ruptured Intracranial Aneurysm Due to Segmental Fibromuscular Dysplasia

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