“…[1][2][3] Associated CHDs include tetralogy of Fallot with or without pulmonary atresia, total anomalous pulmonary venous return, coarctation of aorta, truncus arteriosus, interrupted aortic arch, right atrial isomerism, atrial septal defects, ventricular septal defects (VSDs), pulmonary atresia with VSD, double outlet right ventricle with mitral atresia, and hypoplastic left ventricle. 1,2,[4][5][6][7][8] Aortic arch variants or anomalies such as right-sided aortic arch, high cervical arch, or double aortic arch are frequently associated with this venous anomaly. 1,2,6,9,10 Isolated retroaortic innominate vein without any associated CHD as seen in our patient is exceedingly rare with a reported prevalence of 0.02%.…”