Distraction Osteogenesis in Pierre Robin Sequence and Related Respiratory Problems in Children

Monasterio, Fernando Ortiz; Drucker, Mónica; Molina, Fernando; Ysunza, Antonio

doi:10.1097/00001665-200201000-00018

Cited by 129 publications

(76 citation statements)

References 13 publications

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“…Other series have attained similar results. In 2002, Ortiz-Monasterio et al 10 (n=4) and Denny and Kalantarian 6 (n=5) reported on neonates (aged Ͻ1 month) with PRS and severe upper airway obstruction, all of whom were able to avoid tracheotomy after mandibular DOG.…”

Section: Commentmentioning

confidence: 99%

Mandibular Distraction for Micrognathia and Severe Upper Airway Obstruction

Mandell¹,

Yellon²,

Bradley³

et al. 2004

Arch Otolaryngol Head Neck Surg

121

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To determine whether the use of mandibular distraction osteogenesis (DOG) can help to avoid tracheotomy or achieve decannulation in patients with mandibular hypoplasia and severe upper airway obstruction.Design: Retrospective medical record review (spanning a 27-month period).Setting: Tertiary care children's hospital. Subjects: Group A (n=8) was composed of infants with Pierre Robin sequence and no tracheotomy (mean age, 2.5 months); group B (n = 6), older nontracheotomized micrognathic children with obstructive sleep apnea (OSA) (mean age, 69 months); and group C (n = 12), tracheotomized children with complex congenital syndromes (mean age, 33 months).Intervention: Bilateral mandibular DOG with endoscopic (n = 24) and/or radiographic (n = 17) airway evaluation (mean follow-up, 16 months [range, 2-42 months]).Outcome Measures: Group A, tracheotomy avoidance; group B, resolution of OSA (clinically or on polysomnography); and group C, decannulation.Results: Group A, 7 patients (88%) successfully avoided tracheotomy; group B, 5 patients (83%) had resolution of OSA; and group C, 2 patients (17%) underwent decannulation.Conclusions: Mandibular DOG (1) allows tracheotomy avoidance in infants with isolated Pierre Robin sequence and (2) relieves OSA in older micrognathic children without tracheotomy. However, mandibular DOG does not frequently lead to decannulation in tracheotomized patients with complex congenital syndromes.

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Section: Commentmentioning

confidence: 99%

Mandibular Distraction for Micrognathia and Severe Upper Airway Obstruction

Mandell¹,

Yellon²,

Bradley³

et al. 2004

Arch Otolaryngol Head Neck Surg

121

View full text Add to dashboard Cite

show abstract

“…In 2001, Denny et al [10] demonstrated that mandibular advancement through distraction osteogenesis could improve airway dimensions and result in decannulation in tracheostomy-dependent children. Monasterio [11] and Sidman et al [12], also showed excellent results using distraction to prevent the need for tracheostomy in neonates and children with mandibular hypoplasia with severe tongue-based obstruction.…”

Section: Discussionmentioning

confidence: 95%

Early Mandibular Distraction to Relieve Robin Severe Airway Obstruction in Two Siblings with Lymphedema–Distichiasis Syndrome

Papoff

Castori

Manganaro

et al. 2015

J. Maxillofac. Oral Surg.

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Although micrognathia and cleft palate have been reported in patients with Lymphedema-distichiasis syndrome (LDS), the classic Robin sequence with glossoptosis and airway obstruction has not been previously described in patients with genetically confirmed LDS. Here we report on two female siblings with LDS confirmed by a FOXC2 mutation who presented at birth with severe airway obstruction related to Robin sequence. Respiratory obstruction was successfully managed by early distraction osteogenesis. Our report highlights the unusual occurrence of Robin sequence in LDS patients and advises distraction osteogenesis to resolve breathing problems in LDS patients who present with Robin related severe airway obstruction.

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“…Monasterio [9] and Sidman et al [10], also showed excellent results using distraction to prevent the need for tracheostomy in neonates and children with mandibular hypoplasia with severe tongue-based obstruction. All of these authors used external distraction devices.…”

Section: Discussionmentioning

confidence: 95%

External Mandibular Distraction in Unusual Pediatric Syndromes with Micrognathia and Airway Obstruction

Horta

Marques

Amarante

et al. 2011

J. Maxillofac. Oral Surg.

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Mandibular hypoplasia is a craniofacial malformation that can cause airway obstruction and may affect the eating process. This anomaly is common in many polimalformed Syndromes, including the Pierre Robin Sequence and the Moebius Syndrome. It is also common in cases related to the dysgenesis of the brainstem. In order to avoid tracheostomy, or to allow for early decannulation in severely affected children, external distraction devices were employed in 3 clinical cases to repair mandibular deficiencies. A successful external mandibular distraction induces the removal of the airway obstruction, allowing spontaneous ventilation without devices, an independent eating process with no need of nasogastric or gastrostomy tubes, apart from the linguistic and facial asymmetry improvement.

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Distraction Osteogenesis in Pierre Robin Sequence and Related Respiratory Problems in Children

Abstract: Mandibular distraction is a safe and reliable procedure for treating patients with obstructive sleep apnea.

Cited by 129 publications

References 13 publications

Mandibular Distraction for Micrognathia and Severe Upper Airway Obstruction

Mandibular Distraction for Micrognathia and Severe Upper Airway Obstruction

Early Mandibular Distraction to Relieve Robin Severe Airway Obstruction in Two Siblings with Lymphedema–Distichiasis Syndrome

External Mandibular Distraction in Unusual Pediatric Syndromes with Micrognathia and Airway Obstruction

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