Divertículo vesical congénito y Síndrome de ehlers-danlos: una rara asociación

Burgos, J. Bachiller; Solís, C. Varo; Estudillo, F.; Soto, A. Juárez; Delgado, M. Soto; Aguilar, V. Beltrán; Moreno, D. González; Bernal, C. Sánchez; Rodríguez-Rubio, F; Báez, Johnder

doi:10.1016/s0210-4806(00)72523-x

Cited by 9 publications

(1 citation statement)

References 12 publications

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“…Hutch diverticula cause significant vesicoureteral reflux because they distort the ureterovesical junction 4,5 . Primary congenital diverticula have been linked to the connective tissue disorders known as Ehlers-Danlos types IV, V, and IX, which are said to cause the diverticula to rupture spontaneously 6,7 . Interestingly, a high prevalence of primary bladder diverticula has been linked to Menkes' kinky hair disease, a rare X-linked recessive disorder of copper metabolism 6,7 .…”

Section: Introductionmentioning

confidence: 99%

Resultados clínicos y urodinámicos en divertículos vesicales primarios pediátricos: un estudio comparativo

Karaaslan,

Kuzdan

2024

CIRU

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Objective: This study aimed to compare the effects of bladder diverticula smaller than 30 (SD) mm and larger than 30 mm (LD) on bladder functions and urodynamics. Materials and methods: Our retrospective analysis involved a cohort of 40 pediatric patients diagnosed with primary bladder diverticula. Results: The predicted mean bladder capacity (MBC) was 197.7 ± 95.8 mL, whereas the observed MBC was lower at an average of 170.1 ± 79.6 mL. This indicates that the observed MBC was 88.2 ± 12.9% of the predicted value (percentage). The mean diverticula diameter recorded was 33 ± 19.5 mm, and the diverticula to MBC ratio were calculated to be 0.25 ± 0.18. The distribution of urinary tract infections (UTIs) differed significantly between the groups (p < 0.001). Upper UT dilatation was significantly more common in the LD group (60%, n = 12) than in the SD group (15%, n = 3) (p = 0.003). The mean detrusor pressure (P[detrusor]) was significantly higher in the LD group (137.2 ± 24.1 cm H 2 O) than in the SD group (63.9 ± 5.8 cm H 2 O) (p = 0.001). In addition, the mean peak flow rate (Q max ) was significantly higher in the SD group (20.7 ± 7.9 mL/s) compared to the LD group (12.7 ± 3.8 mL/s) (p < 0.001). Conclusion: Bladder diverticula size is a significant factor in the clinical presentation and management of primary bladder diverticula in pediatric patients.

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