A male Holstein Friesian calf affected with superior cervical ectopia cordis was examined macroscopically and histologically to assess the severity and elucidate other anomalies. This calf died 10 minutes after birth. The heart was round, weighed 380gm, was enveloped in the pericardium, and situated in the swollen part of the ventrocervical region underneath the skin. Inside the spacious pericardial cavity, the heart was characterized by a duplicated and cranioventral apex. The heart was Histologically normal. The cranial vena cava and vena azygos were also duplicated. The sternum was short, especially in the body and xyphoid process. No other anomaly was seen in association with this case.