Double Diastematomyelia

McClelland, Robert R.; Marsh, Donald G.

doi:10.1148/123.2.378

Cited by 9 publications

(3 citation statements)

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“…Multiple accessory neurenteric canals may form two or more noncontiguous SCMs. One or both types of SCM s at different levels have been reported in the same patient [12,13], A large endomesenchymal tract may also cause contigouous SCM s in tandem in which there is no interim normal spinal cord in between the SCM s [1. 2], To our knowledge, such a case containing both types of SCM s at the same level has not been reported.…”

Section: Discussionmentioning

confidence: 99%

Split Cord Malformations: Report of Three Unusual Cases

Erşahin¹,

Demirtaş²,

Mutluer³

et al. 1996

Pediatr Neurosurg

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The unified theory, proposed by Pang et al., explains the embryogenetic mechanisms of all variants of split cord malformations (SCMs). All SCMs originate from one basic error occurring around the time when the primitive neurenteric canal closes. The basic error is the formation of an accessory neurenteric canal between the yolk sac and amnion which is subsequently invested with mesenchyme to form an endomesenchymal tract that splits the notochord and neural plate. Three cases of SCMs which support this unified theory are presented. A 3-month-old girl had a combination of both types of SCMs at the level of T11. The 2nd case, a 2-week-old girl, had type-II SCM associated with a thickened filum terminale, lipomyelomeningocele and ectopic renal tissue within lipoma. A lipomatous tract extending from a subcutaneous lipoma to the intradural fibrous septum contained lymphoid tissues and tubular epithe-lia in a 3-month-old boy with a type-II SCM. These 3 cases support the unified theory.

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Section: Discussionmentioning

confidence: 99%

Split Cord Malformations: Report of Three Unusual Cases

Erşahin¹,

Demirtaş²,

Mutluer³

et al. 1996

Pediatr Neurosurg

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“…The abnormalities in the other opera tive cases are not recorded [15,20,43]. In two autopsy cases a bone spur and two separate dural tubes were found [ 16,19] [6] and two separate bone spurs at sepa rate levels each associated with a DM cleft [27] were also described. (table 9) Twenty-eight patients were treated by surgery.…”

Section: Selection O F Casesmentioning

confidence: 99%

Diastematomyelia in Adults

Russell

Benoit

Joaquin³

1990

Pediatr Neurosurg

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A consecutive series of 45 cases of diastematomyelia in adults is analyzed. The majority of patients were females with a 3.4:1 female to male ratio. The ages ranged from 19 to 76 with a mean of 37.8 years. The lesion was usually located in the lumbar region. In 17 patients the development of symptoms was associated with specific incidents or events, usually trauma. Twelve patients had pre-existing static musculoskeletal or neurologic abnormalities and 20 had cutaneous spinal lesions suggesting dysphraphism. The symptoms and signs included pain and a variety of sensorimotor and/ or sphincteric abnormalities. Metrizamide CT scanning proved to be the most useful diagnostic procedure. Only 4 patients were investigated by MRI and from the information available its role in the diagnosis of adult diastematomyelia is not established. Twenty-three of 24 patients treated by surgery showed marked improvement.

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“…In most of these cases the spurs were not more than three vertebral levels apart. Only one case had widely separated spurs, present at T2 and L3 levels 6. The spur is most commonly found in the lower thoracic or the upper lumbar region and only four case reports of septum above T3 are available in the published literature.…”

Section: Discussionmentioning

confidence: 97%