Double-outlet left atrium: Successful repair of an extremely rare anomaly

Abstract

The clinical detail, echocardiographic features, angiographic evaluation, and surgical repair of double-outlet left atrium (LA) in a 2-year-old boy are discussed. In a solitus position and normally connected systemic and pulmonary venous drainage setting, the only outlet of the right atrium was a secundum atrial septal defect. The LA thus received the entire venous return and then drained into both ventricles through a common atrioventricular valve.

Prenatal diagnosis of double‐outlet left atrium

“…Thirteen other cases of DOLA have been reported in the literature to date, with one case diagnosed prenatally at 20 weeks' gestation and the remaining cases diagnosed postnatally between 20 days and 41 years of age (Table 1) 3,[5][6][7][8][9][10][11][12] .…”