Dyke-Davidoff-Masson Syndrome

Anand, Roshni; Saurya,; Dev, Rahul

doi:10.37549/ar2818

Cited by 2 publications

(3 citation statements)

References 8 publications

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“… 2 Some patients may present with additional symptoms, including cerebellar and basal ganglia atrophy, ear malformations, and neuropsychiatric disorders. 3 , 4 DDMS etiologies are broadly categorized into congenital and acquired. 5 Congenital causes of DDMS include intrauterine vascular injury and cerebral hemispheric hypoperfusion.…”

Section: Introductionmentioning

confidence: 99%

“…DDMS is a clinico‐radiological recognized entity characterized by typical manifestations including drugs resistant epilepsy, intellectual disability, hemiparesis, skull bone thickening associated with cerebral hemiatrophy and hyperpneumatization of paranasal and frontal sinuses on neuroimaging 2 . Some patients may present with additional symptoms, including cerebellar and basal ganglia atrophy, ear malformations, and neuropsychiatric disorders 3,4 . DDMS etiologies are broadly categorized into congenital and acquired 5 .…”

Section: Introductionmentioning

confidence: 99%

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An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient

Djimdé

Yalcouyé

Koita

et al. 2022

Clinical Case Reports

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The Duke–Davidoff–Masson syndrome (DDMS) is a rare neurological condition with unknown prevalence, globally. To date, <100 cases have been reported worldwide. We report the case of an 18‐year‐old patient admitted for status epilepticus seizure, and who presented a right hemiparesis, body asymmetry, joints ankylosis, and mental retardation. Brain CT‐scan revealed left hemisphere atrophy, skull bone thickening, and hyperpneumatization of the frontal sinuses; all consistent with DDMS. Seizures improved remarkably on Levetiracetam and Valproate. This is the first report of an unusual DDMS in Mali, and the diagnosis delay highlights the challenges for the management of these diseases in resource‐limited settings.

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Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

An unusual case of Dyke–Davidoff–Masson syndrome revealed by status epilepticus in a Malian patient

Djimdé

Yalcouyé

Koita

et al. 2022

Clinical Case Reports

View full text Add to dashboard Cite

show abstract

“…2 Some patients may present with additional symptoms including cerebellar and basal ganglia atrophy, ear malformations and neuropsychiatric disorders. 3,4 DDMS' etiologies are broadly categorized into congenital and acquired. 5 Congenital causes of DDMS include intrauterine vascular injury and cerebral hemispheric hypoperfusion and acquired causes mostly derive from birth trauma, periventricular leukomalacia, cerebral hemorrhage, cerebral infarction, cerebral infection, radiation, postictal cerebral hemiatrophy, and prolonged febrile seizures.…”

Section: Introductionmentioning

confidence: 99%