Ebstein's anomaly and intermediate-form atrioventricular septal defect with double-orifice mitral valve

Hartyánszky, István; Lózsádi, K; Kádár, Krisztina; Hüttl, Tivadar; Király, László

doi:10.1016/s0022-5223(19)34657-4

Cited by 8 publications

(3 citation statements)

References 4 publications

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“…In the other 50%, it can cause clinically significant mitral stenosis or mitral regurgitation. The commonly associated lesion is atrioventricular septal defect, aortic coarctation, interrupted aortic arch, patent ductus arteriosus, primum atrial septal defect, tetralogy of Fallot, and Ebstein anomaly [ 3 , 4 ]. In our case, double orifice mitral valve is associated to ventricular septal defect, aortic coarctation and bicuspid aortic valve.…”

Section: Discussionmentioning

confidence: 99%

Unusual findings in secondary hypertension: double orifice mitral associated to aortic coarctation, bicuspid aortic valve, and ventricular septal defect

Mouine¹,

Amri²,

Cherti³

2014

Int Arch Med

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Double orifice mitral valve is a rare congenital anomaly presenting as the division of the mitral orifice into two anatomically distinct orifices, it is most often associated with other congenital heart defects such as left-sided obstructive lesions, ventricular septal defects or aortic coarctation. We report the case of a 15 year’s old boy, admitted for arterial hypertension, auscultation revealed a rude aortic systolic murmur. Femoral pulses were weak. Owing to the suspicion of aortic coarctation, transthoracic echocardiography was performed, the aortic coarctation with dilation of the aorta proximal to the stenosis was confirmed and bicuspid aortic valve was found with good function. The mitral valve was dysmorphic, having two orifices; it was divided into 2 separate valve orifices by a fibrous bridge. No mitral or aortic regurgitation was documented by color Doppler flow imaging. The left ventricular ejection fraction was normal. There was a small peri membranous ventricular septal defect with left to right shunt. Owing to the severity of the aortic coarctation and taking into account the anatomy and characteristics of the patient, he was made a surgical correction of aortic coarctation with good outcome.

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Section: Discussionmentioning

confidence: 99%

Unusual findings in secondary hypertension: double orifice mitral associated to aortic coarctation, bicuspid aortic valve, and ventricular septal defect

Mouine¹,

Amri²,

Cherti³

2014

Int Arch Med

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“…A DOMV occurs either as an isolated abnormality or in association with other congenital cardiac anomalies such as an atrioventricular septal defect, 1,6 coarctation of the aorta, 7 Ebstein anomaly, 8 tetralogy of Fallot, 9 tricuspid atresia, 10 and left ventricular noncompaction. 11,12 An atrioventricular septal defect is the most common associated lesion.…”

Section: Discussionmentioning

confidence: 99%

Isolated Double-Orifice Mitral Valve Anomaly on 3-Dimensional Transesophageal Echocardiography

Han

He²,

Li³

et al. 2009

Journal of Ultrasound in Medicine

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“…Ritka fejlődési rendellenesség a "double orifice" mitralis billentyű, amikor egy nagyobb és egy kisebb elszeparálódott mitralis billentyű található. Ezek inkább szűkületet, mint regurgitatiót okoznak, de minden esetben egyedileg kell dönteni sorsukról a hemodinamikát befolyásoló szerepük alapján: a) nem kell vele foglalkozni, b) plasztikázni kell, c) műbillentyűre kell cserélni[4,5]. 2.…”

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A mitralis billentyű sebészete atrioventricularis septumdefektusban

Hartyánszky

Bogáts

2021

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Összefoglaló. A veleszületett szívbetegségek egyik gyakori formáját jelentő atrioventricularis septumdefektus korrekciós műtétjének kritikus pontja a közös atrioventricularis szájadék elválasztásával a mitralis billentyű kialakítása. A korrekció sikere számos anatómiai variáns függvénye, ezért nem lehet minden esetben a tökéletes anatómiai viszonyokat kialakítani. A fennmaradó billentyűstenosisok, regurgitatiók a későbbi életkorban progressziót mutatva olyan hemodinamikai kórképeket, keringési elégtelenséget okozhatnak, melyek további beavatkozásokat igényelhetnek. A mitralis billentyűnek az atrioventricularis septumdefektushoz társuló betegsége koraszülöttkortól aggkorig minden életkorban előfordul, más-más műtéti megoldást igényelve. A szerzők részletezik a különböző életkorokra vonatkozóan a napjainkban lehetséges és szükséges műtéti megoldásokat, sebészi kihívásokat. A mitralis billentyű műbillentyűre történő cseréjében a klasszikus sebészi megoldások mellett napjainkban új beavatkozásokként jelentős számban jelentkeznek a katéteres intervenciós és hibrid megoldások. A felnőttkort egyre nagyobb számban megélő betegek fokozott odafigyelést, speciális ellátást igényelnek a kardiológusoktól, szívsebészektől. Orv Hetil. 2021; 162(35): 1397–1401. Summary. The critical point of the atrioventricular septal defect correction is to separate the common atrioventricular orifice, which results in the reconstruction of the mitral valve. The success of the correction depends on many anatomical aspects, therefore a perfect anatomical outcome is not always possible. The remaining valvular stenoses and regurgitations, showing progression at a later age, may result in hemodynamic disorders and circulatory insufficiency that may require further interventions. Mitral valve disease associated with atrioventricular septal defect occurs at all ages from preterm to adulthood, requiring different surgical solutions. The authors detail the possible and necessary surgical solutions and surgical challenges at different ages. In addition to the classic surgical solutions, a significant number of catheter interventional and hybrid solutions are emerging as new interventions in the replacement of the mitral valve with an artificial valve. An increasing number of patients living in adulthood require increased attention and special care from cardiologists and cardiac surgeons. Orv Hetil. 2021; 162(35): 1397–1401.

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Ebstein's anomaly and intermediate-form atrioventricular septal defect with double-orifice mitral valve

Cited by 8 publications

References 4 publications

Unusual findings in secondary hypertension: double orifice mitral associated to aortic coarctation, bicuspid aortic valve, and ventricular septal defect

Unusual findings in secondary hypertension: double orifice mitral associated to aortic coarctation, bicuspid aortic valve, and ventricular septal defect

Isolated Double-Orifice Mitral Valve Anomaly on 3-Dimensional Transesophageal Echocardiography

A mitralis billentyű sebészete atrioventricularis septumdefektusban

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