Ebstein's anomaly: repair based on functional analysis

Abstract

Conservative surgery is indicated for all symptomatic patients. The incidence of valve repair is high when leaflet mobilization is performed. Valve replacement can be avoided in most cases. Functional and hemodynamic results are excellent.

Ebstein’s Anomaly

“…This repair was reported in 191 patients (meanϮSD age, 24Ϯ15 years). 64 The early mortality rate was 9%, and the mean late survival rate at 20 years was 82%Ϯ5%. It is unclear whether late problems will develop because of devitalized tricuspid valve tissue related to reattachment.…”

ESC Guidelines for the management of grown-up congenital heart disease (new version 2010)

“…A conservative therapy can alleviate symptoms temporarily and create a beneficial basis for the following operation. 78 Oral anticoagulation is recommended for patients with a history of paradoxical embolism or atrial fibrillation. Symptomatic rhythm disorders can be treated conservatively or, preferably, with EP intervention.…”

A técnica do cone para correção da anomalia de Ebstein: resultados imediatos e em longo prazo

“…The two series, however, had different characteristics as our patients were younger and had a lower cardiothoracic index than those in the series by Chauvaud et al 20 .…”

“…This strategy of right ventricular decompression made the cavopulmonary shunt unnecessary in our patients. In this sense, Chauvaud et al 20 reported better results with the use of bidirectional cavopulmonary anastomosis, together with Carpentier's operation, in patients with severe right ventricular dysfunction. These authors used this technique in 36% of patients in order to reduce right ventricular preload in cases of severe right ventricular dysfunction, thus obtaining a significant reduction in mortality caused by right ventricular failure.…”