Echocardiographic diagnosis of total or left congenital pericardial absence with positional change

Kim, Min Jeong; Jung, Ji Hyun; Yoon, Yeonyee E.; Kim, Hack‐Lyoung; Park, Jun Bin; Lee, Seung–Pyo; Kim, Yong Jin; Cho, Goo Young; Oh, Jae K.

doi:10.1136/heartjnl-2016-310870

Cited by 7 publications

(4 citation statements)

References 21 publications

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“…CPDs have also been noted in patients with VATER syndrome and Pallister-Killian syndrome 12 15. ASD shares many clinical features and ECG findings with CPD, such as systolic ejection murmur, wide split of S2 and RBBB ECG pattern 16. Both conditions can be differentiated by the positional changes during TTE in patients with CPD 16.…”

Section: Discussionmentioning

confidence: 99%

“…ASD shares many clinical features and ECG findings with CPD, such as systolic ejection murmur, wide split of S2 and RBBB ECG pattern 16. Both conditions can be differentiated by the positional changes during TTE in patients with CPD 16. The majority of the cases are asymptomatic and are frequently diagnosed incidentally postmortem1 or when undergoing cardiac surgery 2…”

Section: Discussionmentioning

confidence: 99%

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Case series, contemporary review and imaging guided diagnostic and management approach of congenital pericardial defects

et al. 2020

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ObjectiveCongenital pericardial defect (CPD) is a rare entity with an estimated frequency of 0.01%–0.04%. The recognition of this anomaly is important since it can be associated with serious complications. The aim of this study and review was to describe clinical and imaging features that help in establishing the diagnosis of this condition.MethodsWe retrospectively reviewed all adult patients at the Cleveland Clinic Health System with the diagnosis of CPD between the years 2000 and 2015. Baseline clinical characteristics, clinical manifestations, ECG, transthoracic echocardiography (TTE), cardiac CT and cardiac magnetic resonance (CMR) images were reviewed.ResultsEight patients were included in the study. Sixty-three percent of patients were males with mean age at diagnosis of 48 years, 63% had a partial pericardial defect on the left side and right ventricular (RV) dilation on TTE. Three patients had CMR. Levocardia was present in all CMRs. One patient had greater than 60° clockwise rotation and none of the CMRs showed ballooning of the left ventricular apex. One patient required surgical pericardioplasty. The remaining seven patients had a median follow-up of 17.3 months (5–144.9 months) and all remained asymptomatic.ConclusionCPDs are more likely to be partial on the left side and patients often have RV dilation on the TTE and levocardia on CMR. Most patients remain stable and do not require surgical intervention. TTE and CMR play an important role in making the diagnosis of this anomaly.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Case series, contemporary review and imaging guided diagnostic and management approach of congenital pericardial defects

et al. 2020

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“…Therefore, lack of visibility of the pericardium on cardiac MRI or CCT does not prove the absence of the pericardium. Positional change is a simple and reliable intervention for echocardiographic diagnosis of CAP [4]. Although the diagnostic usefulness of decubitus imaging in CAP with CCT has been reported, it requires a double radiation dose [5].…”

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Left-sided congenital absence of pericardium confirmed by decubitus cardiac magnetic resonance imaging

Yoshihara,

Yaegashi,

Matsunaga

et al. 2024

Pol Heart J

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“…Although CT and magnetic resonance imaging are the gold standard for diagnosing CAP, 4 certain findings on an ECG, echocardiography, and chest x-ray can also indicate its presence. 2 Nevertheless, the rarity of CAP can make it difficult to detect; therefore, clinicians should familiarize themselves with the different findings that can lead to a prompt diagnosis.…”

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confidence: 99%

Snoopy’s Heart: A Case of Complete Congenital Absence of the Pericardium

Vosko

Zhan

Nabi

et al. 2019

Methodist DeBakey Cardiovascular Journal

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Echocardiographic diagnosis of total or left congenital pericardial absence with positional change

Abstract: Patients with CAP have dynamic alteration in cardiac position depending on posture, which is not observed in ASD or in normal controls. Hence, total or left-sided CAP can be reliably diagnosed with positional changes during routine echocardiography.

Cited by 7 publications

References 21 publications

Case series, contemporary review and imaging guided diagnostic and management approach of congenital pericardial defects

Case series, contemporary review and imaging guided diagnostic and management approach of congenital pericardial defects

Left-sided congenital absence of pericardium confirmed by decubitus cardiac magnetic resonance imaging

Snoopy’s Heart: A Case of Complete Congenital Absence of the Pericardium

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