eComment: Cor triatriatum and cardiac hemolytic anemia

Edwin, Frank; Aniteye, Ernest; Entsua-Mensah, Kow; Frimpong-Boateng, K.

doi:10.1510/icvts.2008.201293a

Cited by 1 publication

(1 citation statement)

References 3 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Shear stress significant enough to cause hemolysis was met in our case; however, it was not met in another such case study by Mahmoud et al (2009), which revealed clinically significant anemia despite having a low shear stress through the membranous septum in an infant with cor triatriatum sinister. Thus, there are other hydrodynamic mechanisms, other than shear stress alone, that are likely involved in causing significant hemolysis and subsequent anemia, including orifice size of the defect and the degree of the pressure gradient through the defect (Edwin, Anitieye, Entsua-Mensah, & Frimpong-Boateng, 2009).…”

Section: Discussionmentioning

confidence: 99%

Shear Stress Causing Hemolytic Anemia and Congestive Heart Failure as an Initial Presentation of Cor Triatriatum in an Infant

Meyer

Quirk

Pick

et al. 2021

Advanced Emergency Nursing Journal

View full text Add to dashboard Cite

Among congenital cardiac defects, cor triatriatum sinistrum is a rare formation of 3 distinct atrial chambers in the heart. Depending on the size of the defect in the membranous septum, the symptoms can range from asymptomatic to severe pulmonary hypertension. Individuals can go years, sometimes to the second and third decades of life, before presenting with symptoms. Although it is well known to be associated with pulmonary veno-occlusive disease, the association with hemolytic anemia is much less well known. Identifying the subtle signs and symptoms of cor triatriatum in the emergency department can save a life. Here, we present the case of a 6-month-old infant with hemolytic anemia in the setting of right-sided congestive heart failure leading to the diagnosis of cor triatriatum. Anemia developed secondary to shearing stress caused by the heart defect itself. Complete resolution of symptoms occurred status post septectomy and repair of the defect.

show abstract

Section: Discussionmentioning

confidence: 99%