Ectopic Vas Deferens Inserting Into Distal Retroiliac Ureter in the Currarino Syndrome

Alonso, Vicente Gutiérrez; Pérez, Sonia; Barrero, Rafael; García-Merino, Francisco

doi:10.1016/j.urology.2016.05.020

Cited by 2 publications

(6 citation statements)

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“…When the duplication occurs at the superior end of the mesonephric duct, the polyorchidisim associated with duplicated ductus deferens [ 4 ]. In addition, the embryological reason for the insertion of the ductus deferens into the ureter is the failure of obliteration of the potion of the Wolffian duct that receives both the ureter and the ductus deferens, which results in ectopy ductus deferens into the ureter [ 2 ]. Histologically, the specimen shows a tubal structure having a thick muscle coat and lined by almost completely eroded epithelium with edema and inflammation in the subepithelial connective tissue.…”

Section: Discussionmentioning

confidence: 99%

“…The clinical presentation of this case includes anus atresia, hypospadias with undescended testes, infertility, swollen scrotum, hematuria, and urinary tract infection [ 7 ]. The retrograde passage of urine into the vas deferens can cause epididymitis and even scrotal abscesses when associated with hydroureter because of vesicoureteral reflux or obstruction [ 2 ]. Radiological study of the bladder and ureters by retrograde uretro-pyelography is the procedure most likely to confirm the diagnosis.…”

Section: Discussionmentioning

confidence: 99%

“…In general, Ductus deferens' precise etiology is still unknown. Patients may be asymptomatic or complaining of urinary tract infections and/or epididymitis [ 2 ]. The insertion of Ductus deferens into the Ureter is a rare congenital malformation.…”

Section: Introductionmentioning

confidence: 99%

“…The insertion of Ductus deferens into the Ureter is a rare congenital malformation. Most of these cases are associated with renal dysplasia [ 2 ]. The diagnosis should be confirmed by Cystourethroscopy catheterization and retrograde urethrogram, but the definitive diagnosis is done by vasography [ 2 ].…”

Section: Introductionmentioning

confidence: 99%

“…Most of these cases are associated with renal dysplasia [ 2 ]. The diagnosis should be confirmed by Cystourethroscopy catheterization and retrograde urethrogram, but the definitive diagnosis is done by vasography [ 2 ]. Curative management is preferred to be complete surgical severance of the pathological urogenital connection [ 3 ].…”

Section: Introductionmentioning

confidence: 99%

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Multiple vas deferens with polyorchidism and many congenital malformations in a symptomatic 11-year-old male patient: a rare case report

Mansour¹,

Ismail

Dashan

et al. 2022

BMC Urol

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Background Ductus deferens may manifest in a variety of anomalies such as its absence, duplication, ectopy, or diverticulum. Ectopic seminal tract opening has two main types, ectopic ejaculatory duct opening, and ectopic vas deferens opening. Generally, ductus deferens anomalies affect approximately 0.05% of the population. Patients may be asymptomatic or complaining of urinary tract infections and/or epididymitis. Most of these cases are associated with renal dysplasia. To confirm the diagnosis Cystourethroscopy catheterization and retrograde urethrogram should be performed, but the definitive diagnosis is done by vasography. The definitive treatment is complete surgical resection of the pathological urogenital connection. This case is commonly discovered while exploring other findings such as testicular torsion and inguinal hernia. Case presentation We report a rare case of an 11-year-old male who presented with gross hematuria and numerous congenital malformations including a left polydactyly clubfoot, polyorchidism, with several surgical procedures, and left kidney dysgenesis. Surgery was performed for a left inguinal hernia, during which a third undescended testicle was discovered incidentally and was eradicated. A retrograde urethrogram was performed to establish the diagnosis. A fistula- that is connected with the left ureter- was resected. The histopathologic findings confirmed the diagnosis of true duplication of the Vas deferens, with communication between the ureter and the vas deferens. By follow-up, the kidney function tests were within normal limits. Conclusions This case report aims to highlight the early diagnosis and management of the duplicated vas deferens and the associated congenital malformations to improve the prognosis and kidney function and to avoid long-term complications.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%