Embolizaço percutânea de fístulas arteriovenosas pulmonares em paciente com telangiectasia hemorrágica hereditária

Abstract

Most cases of pulmonary arteriovenous malformations occur in patients with hereditary hemorrhagic telangiectasia. It is a rare disease that may present with strokelike symptoms in young patients. With the development of occlusion devices, percutaneous embolization has become the treatment of choice. We report a case of a 33 year-old man with a history of multiple strokes, cyanosis, dyspnea, recurrent epistaxis and high flow pulmonary fistulae who was submitted to percutaneous embolization. The patient improved clinically and has had no recurring symptoms in the 30-month follow-up.