Embryonic paratesticular rhabdomyosarcoma: a case report

Abstract

IntroductionAn embryonic paratesticular rhabdomyosarcoma is a very rare mesenchymal tumor. It is an intrascrotal tumor that is localized in paratesticular structures such as the epididymis or spermatic cord. Rhabdomyosarcoma is most often observed in children and adolescents, presenting as a painless scrotal mass.Case presentationOur patient was an 18-year-old Moroccan man who presented with a painless left scrotal mass that had evolved over four months. An inguinal orchiectomy was performed. A histological examination of the excised tissue revealed an embryonic rhabdomyosarcoma.Our patient had three sessions of chemotherapy with vincristine, actinomycin C and cyclophosphamide. Each chemotherapy session was conducted over five days, with a cycle of 21 days. Our patient was assessed two months after the last chemotherapy session and demonstrated good clinical improvement.ConclusionParatesticular rhabdomyosarcoma is a rare aggressive tumor manifesting in children and very young adults. Localized forms have a good prognosis whereas metastatic tumors show very poor results. A well-defined treatment based on surgery and chemotherapy yields good results.

Synchronous rhabdomyosarcoma of the testis and kidney: A case report and review of the literature

“…1,2,4,5 Most reviews document a male preponderance and a bimodal peak age pattern. 3,4,[6][7][8] Although more than half of the cases occur within the first decade of life, the second smaller frequency peak is seen mainly in males. [1][2][3]6 RMS can occur in any part of the body due to its embryonal mesenchymal origin and mimics the characteristics of striated muscles.…”

“…Rhabdomyosarcoma (RMS) is the commonest soft tissue sarcoma in both children and adolescents representing 40% of such tumours in North America and more than 50% in Africa. [1][2][3][4][5] Most reviews document a male preponderance and a bimodal peak age pattern in the first and 5th decades of life 3,4,7,8,6 .…”

Rhabdomyosarcome embryonnaire paratesticulaire : à propos d’un cas et revue de la littérature

“…Il s'agit de l'unique cas de rhabdomyosarcome para-testiculaire traité dans notre institution parmi les patients qui y ont été pris en charge durant 20 ans. Dans la littérature, la majorité des publications traitent des cas isolés [4,5].…”

Rhabdomyosarcoma of spermatic cord in a 65-year-old man presenting as a groin swelling

“…Incidence of these tumours is highest in the younger age groups, with two frequency peaks—one at around 4 years of age, and another, at around 18 years of age. In fact, RMS is the most common soft tissue sarcoma of childhood 3. It rarely appears after second decade 4…”

“…If there is fixation of tumour to the scrotal wall, hemiscrotectomy is an additional procedure to be performed. In case of suspected nodal involvement, CT of pelvis can be used to confirm, before inguinal lymphadenectomy 2 3. However, local recurrence is frequent.…”