Enchondromatosis (Ollier disease)

Insights into Enchondroma, Enchondromatosis and the risk of secondary Chondrosarcoma. Review of the literature with an emphasis on the clinical behaviour, radiology, malignant transformation and the follow up

“…Enchondromatosis encompasses several different subtypes of which Ollier disease (enchondromatosis) ( Figure 2) and Maffucci syndrome (enchondromatosis associated with soft tissue haemangiomas) ( Figure 3) are most common [7,8]. Other subtypes such as metachondromatosis, genochondromatosis, spondyloenchondrodysplasia, dysspondyloenchondromatosis and cheirospondyloenchondromatosis are rare [5,7].…”

Five Polyostotic Conditions That General Orthopedic Surgeons Should Recognize (or Should Not Miss)

“…In the phalanges, enchondromata may extend to the ends of bones. 7 In hands and feet, these lesions may appear more aggressive radiologically but are generally considered benign. In the long bones, radiolucent streaks or fan-like septations extending from the growth plate into the diaphysis and asymmetric enlargement and flaring of the metaphyses may be present in patients with multiple enchondroma (Fig.…”