Endorectal pull-through procedure for Hirschsprung's disease with and without primary anastomosis

Faecal composition after surgery for Hirschsprung's disease.

“…Three-day, urine-free faecal collections were performed on 14 healthy children, mean age 5 years (range 2-9 years) and on 17 patients who had undergone the modified Soave endorectal pull-through operation (Soave, 1964;Boley et al, 1968). Fig.…”

Hirschsprung’s Disease: Diagnosis and Management

“…HD is rarely diagnosed in older children or adults. [1][2][3][13][14][15][16][17] HD has previously been recognized as being rare or absent in premature babies. More recent reports indicate a rising prevalence in premature babies.…”

“…Ganglion cells are present in rectum, but the rectal motility is abnormal. 2,3,7,9 Presentation HD usually presents in infancy, although some patients present later in life. Symptoms range from neonatal intestinal obstruction to chronic progressive constipation in older children (Table I).…”

“…Three definitive surgical procedures commonly performed for HD: (a) Swenson procedure (removal of aganglionic portion of colon), (b) Duhamel procedure (retro-rectal anastomosis), and (c) Soave procedure (endorectal pull-through). 2,7,17 All three techniques can be done with open abdominal incisions or laparoscopic-assisted procedure. They can be done as two-stage (with an initial diverting colostomy) or as single-stage.…”

“…The aganglionic segment includes the distal rectum and a variable length of contiguous proximal intestine. [1][2][3][4] Hirschsprung's disease was first described by Frederick Ruysch in 1691 as the phenomena of an extremely dilated colon. 5,6 First comprehensive description was given by Harold Hirschsprung, a pediatrician from Copenhagen, Denmark at the Society of Pediatrics in Berlin in 1886.…”