“…[4] reported the first case of ECIPAS; and since then 33 articles and 36 patients have been reported in the English language literature (Table
1), suggesting the rarity of the disease. However, the exact incidence of ECIPAS is difficult to determine as over 50% of the cases were incidentally detected
[8,9,12,14,15,18,19,22-24],
[26,27,30,32,34]. The mean age of the patients was 46.1 years (range 12 to 70 years), with a female preponderance (58.3%)
[6,7,10-13,16,17,19-21,24-26,28],
[31,33,34,36].…”