Enfermedad de la motoneurona

Gálvez, P. García; Cambón, R. Sebastián; Pascual, F. Higes; Sánchez-Migallón, M. J.; Izquierdo, A. Yusta

doi:10.1016/s0304-5412(11)70079-8

Cited by 3 publications

(7 citation statements)

References 31 publications

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“…Esta enfermedad genera un importante cambio en la estructura y dinámica familiar con problemas emocionales, psicológicos y económicos que requieren respuestas ágiles, coordinadas y accesibles para el enfermo y el entorno familiar. Al ser una enfermedad degenerativa e invalidante es de vital importancia el seguimiento y coordinación por parte del equipo de Atención Primaria [1][2][3][4][9][10][11] .…”

Section: Discussionunclassified

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Esclerosis Lateral Amiotrófica, presentación atípica

Juárez

Céspedes

Honor³

et al. 2015

Rev Clin Med Fam

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La esclerosis lateral amiotrófica (ELA) es una enfermedad neurodegenerativa, progresiva, con desenlace fatal, que afecta a neuronas motoras de la médula espinal, tronco cerebral y corteza motora. Se produce un fracaso del sistema motor que dirige, regula y mantiene la musculatura esquelética, responsable de la capacidad para moverse y relacionarse con el entorno. Presentamos el caso de un hombre de 58 años de edad con diagnóstico de ELA, con sintomatología inicial atípica que dificultó el juicio clínico final, resaltando en el diagnóstico diferencial la miopatía por cuerpos de inclusión.

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Section: Discussionunclassified

“…Existen focos endémicos con mayor prevalencia en regiones del Pacífico Occidental con una incidencia de 50-150 veces superior; en cambio, es menor en la población africana, asiática e hispánica. La mayoría de los pacientes con ELA fallecen por fallo respiratorio, generalmente entre 3 y 5 años desde el inicio de los síntomas [1][2][3][4] .…”

Section: Introductionunclassified

Esclerosis Lateral Amiotrófica, presentación atípica

Juárez

Céspedes

Honor³

et al. 2015

Rev Clin Med Fam

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“…The mean evolution time of our cases was short (3.5 months), we observed those patients at the onset of disease. Authors report an evolution time about 3-5 years [1][2][3]5,7,8]. ALS is a severely life-shortening condition for most people.…”

Section: Evolution Timementioning

confidence: 99%

“…It's agree with others reports. Muscular atrophy is one of the most common sign reported in ALS [5,7,8]. Muscle bulbar weakness was observed only in two patients.…”

Section: Clinic Signsmentioning

confidence: 99%

“…There are no specific tests to diagnose ALS, but neurophysiological studies are a basic tool for ALS diagnostic. Imaging studies, especially Magnetic Resonance Image (MRI) is very useful to differentiate ALS from others diseases, like multiple sclerosis, cervical spondylosis, cord tumor, syringomyelia, that could be similar to ALS [7][8][9].…”

Section: Introductionmentioning

confidence: 99%

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ALS Diagnostic in the Electrodiagnostic Department of an Orthopedic Hospital during 2014-2015. Clinical and Electrophysiological Characteristic

Hernández¹

2016

OAJNN

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Introduction: Amyotrophic Lateral Sclerosis (ALS) is an uncommon illness, it is caused by motor neuron degeneration; upper, lower and bulbar muscles are affected. The diagnostic is based in Scorial criteria. In some cases it needs to be differentiating from orthopedic illness. ALS diagnosis in electrodiagnostic lab of "Frank Pais" orthopedic hospital has been 2-3 patients per year in the last 5 years.Method: During January 2014-January 2015, nine patients were evaluated, four of them had ALS diagnosis and the other five were diagnosed like orthopedic illness. Sensory and by segments motor nerve conduction studies, electromyography, somato-sensory evoked potentials (SSEP) and Magnetic Resonance Image (MRI) were done to them. Results:The age of patients was from 30-60 years old. Eight of them were male and one was female. Illness started in upper extremities in 55.5% of patients; it was in concordance with percent of muscle atrophy at physical exam. Clinical fasciculation were present in all patients, in 22.2% bulbar muscle were affected. Hyperreflexia was present in 44.4% and plantar reflex was abnormal in 100 %. Nerve conduction was abnormal in 77.7%, SSEP were abnormal in 44.4% and EMG abnormalities were observed in 100% of patients. MRI was abnormal in 66.6%, it showed not specific abnormalities.Conclusions: ALS patients increased in electrodiagnostic lab of orthopedic "Frank Pais" hospital in relation to previous five years. Almost patients had initial orthopedic illness diagnosis. Electrophysiological and image studies confirmed ALS diagnosis in 100% of cases.

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Amyotrophic Lateral Sclerosis can Mimic Orthopedic Disease - Cases Report

Hernández¹

2015

OAJNN

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Enfermedad de la motoneurona

Cited by 3 publications

References 31 publications

Esclerosis Lateral Amiotrófica, presentación atípica

Esclerosis Lateral Amiotrófica, presentación atípica

ALS Diagnostic in the Electrodiagnostic Department of an Orthopedic Hospital during 2014-2015. Clinical and Electrophysiological Characteristic

Amyotrophic Lateral Sclerosis can Mimic Orthopedic Disease - Cases Report

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