Epignathus teratoma with bifid tongue and median glossal salivary mass: report of a case

Medial tongue cleft associated with intraoral hamartoma—case report and review of literature

“…Median tongue clefts are reported in the literature to be associated with median lip clefts or median mandibular clefts 5,6,8,[10][11][12]14,16,17,19 . Median tongue or lip clefts are described also as being associated with orofacial digital syndromes Type I 8,16,17 , Type II (Mohr syndrome) 8,10,12,14 , Type IV (Mohr-Majewski syndrome) 5,11,14 and Type VI (Varadi syndrome) 14,19 .…”

Congenital Facial Teratoma

“…The lesion was enucleated and showed no recurrence after 18 months [4]. Congenital epignathus teratoma which occurs in approximately 1:35,000-1:200,000 live births, where major concern are airway obstruction and facial distortion are reported in the literature [2][3][4][5].…”

“…Depending on the location, size and histological grade, a teratoma carries a mortality rate of 80-100% in which the tumor mass impinges on the airway [3,5,7].…”

“…These tumors are frequently associated with other congenital anomalies with in head and neck such as cleft palate, bifid tongue and bifid uvula [2,3].…”

Giant Epignathus Teratoma Involving the Palate, Tongue, and Floor of the Mouth

“…1 Epignathus is a rare congenital nasopharyngeal malformation classified as a mature teratoma, in which the infant is born with a mass of tissues protruding from the mouth. 12,13 These can be small, interfering with feeding, 14 or massive, leading to an appreciable risk of obstruction of the upper airway and death soon after birth. 15,16 The mass lesion arises from the upper jaw, palate, and sphenoid bone.…”