Epithelioid Angiosarcoma of the Aorta in a 47-Year-old Man: A Case Report and Literature Review

Dehqanzada, Zia A.; Menezes, Geetha; Mukherjee, D

doi:10.1016/j.jsurg.2007.01.025

Cited by 12 publications

(9 citation statements)

References 37 publications

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“…Epithelioid angiosarcomas are considered as especially aggressive tumors, with metastases reported in skin, mesentery, brain, liver, kidney, spleen, bones, lungs, adrenal glands [7,8,[13][14][15], and sometimes in the small bowel [2]. Aortic sarcomas show an intraluminal growth pattern and leave the media intact, as can also be nicely seen in the ultrasound imaging of our patient.…”

Section: Discussionsupporting

confidence: 66%

“…Aortic tumors are exceedingly rare: a recent comprehensive review reported only 223 of all sorts of malignant aortic tumors in world literature between 1873 (first description) and 2017 [1]. Epithelioid angiosarcoma, again a rather rare histological subtype of aortic wall tumors, is described as occuring mostly (70 %) in men with a median age of 62 years [2].…”

Section: Discussionmentioning

confidence: 99%

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An Unusual Case of Iron-Deficiency Anemia: The Culprit Hides in the Aorta

et al. 2020

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In a 72-year-old patient with anemia (Hb 7 g/dl), duodenoscopy exhibited an area of polypous irregular-looking mucosa. Histology revealed duodenal infiltration by epithelioid tumor cells, immunhistochemically positive for endothelial cell markers (CD34, CD31, ERG). Ultrasonography showed thrombotic material in the otherwise unremarkable abdominal aorta with some uptake of contrast bubbles on CEUS. Histological and clinical diagnosis assumed an epithelioid angiosarcoma of the thoraco-abdominal aorta at the level of the visceral and renal arteries with duodenal metastases.To prevent further shedding of tumor cells and aortic rupture, a branched stent-graft was placed into the thoraco-abdominal aorta. Palliative chemotherapy with gemcitabine and docetaxel was started, leading to a partial remission after 6 cycles. Three months later, however, there was a progress of the duodenal masses with new pulmonal and osseous metastases. Thirteen months after the initial diagnosis, death occured due to a hemorrhagic shock caused by a hematothorax.Aortic tumors are exceedingly rare, with only slightly more than 220 cases reported so far. In most cases, diagnosis is made either at autopsy or after an emergency operation for embolic complications like embolic intestinal ischemia. With an overall median survival of 8 months, prognosis is very poor.This case sensitizes for the correct sonographic interpretation of aortic “thrombi” in an otherwise normally appearing aorta, possibly with the aid of CEUS. Besides, it demonstrates the relatively early and uncommon diagnosis of an aortic angiosarcoma by the combination of endoscopy, immunohistochemistry, and ultrasonography.

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Section: Discussionsupporting

confidence: 66%

Section: Discussionmentioning

confidence: 99%

An Unusual Case of Iron-Deficiency Anemia: The Culprit Hides in the Aorta

et al. 2020

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“…1-3 Others suggest that an en bloc resection of the affected aorta with interposition graft placement should be performed ideally. 4,5 Our analysis showed that patients undergoing en bloc resection had worse median survival, but better mean survival. Our conclusions are limited, however, by the small numbers of cases that have been reported of this very rare tumor.…”

Section: Discussionmentioning

confidence: 80%

Postoperative outcomes in intimal aortic angiosarcoma: A case report and review of the literature

Nicotera

Simosa²,

Campbell³

2009

Journal of Vascular Surgery

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“…Other primary sites that have been reported included skin, spleen, nervous system, gastrointestinal tract and bone. Case reports of angiosarcoma arising ovaries, prostate, adrenal gland, vagina and aorta have also been described [1][2][3][4][5][6][7]. Epithelioid angiosarcoma involving the lung is a rare disorder with low incidence, especially its primary form.…”

Section: Angiosarcomas Are a Type Of Malignant Vascular Tumour Characmentioning

confidence: 99%

Epithelioid Angiosarcoma of the Lung with Pleural Metastases: A Rare Cause of Haemoptysis

Carillo¹,

Carretero²,

Vázquez³

et al. 2010

Heart, Lung and Circulation

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Epithelioid Angiosarcoma of the Aorta in a 47-Year-old Man: A Case Report and Literature Review

Cited by 12 publications

References 37 publications

An Unusual Case of Iron-Deficiency Anemia: The Culprit Hides in the Aorta

An Unusual Case of Iron-Deficiency Anemia: The Culprit Hides in the Aorta

Postoperative outcomes in intimal aortic angiosarcoma: A case report and review of the literature

Epithelioid Angiosarcoma of the Lung with Pleural Metastases: A Rare Cause of Haemoptysis

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