“…It arises from the dilator and sphincter muscles, which are of neuroectoderm in origin. Ebstein-Barr virus has been intimately associated, though not necessarily in a causal fashion, with multiple malignancies in AIDS including Burkitt's lymphoma, nasopharyngeal carcinoma, Hodgkin's disease, B-cell lymphomas [1], and leiomyosarcoma [4,5,7,8]. Although intraocular leiomyosarcoma has a potential to spread locally, it rarely metastasizes to distant organs resulting in an excellent survival prognosis [9].…”