Esophageal atresia and hypertrofic pyloric stenosis: An association to consider

Abstract

Esophageal atresia (EA) with distal tracheosophageal fistula (TEF) develops hypertrophic pyloric stenosis (HPS) during the late postoperative period with a described prevalence of 1%-10%.The aim of this retrospective study is to show our experience in this association and to report two specific cases. Of 61 patients with EA treated in our institution, 2 developed HPS. Both cases underwent a Ramstedt extramucosal pyloromyotomy. Currently, patients are asymptomatic.Our frequency (3.3%) is similar to other publications, about 1%-10%. It is important to be aware of this association in a patient with a history of EA and recurrent vomiting in the late postoperative period. The etiology of this association should be investigated.

Hypertrophic pyloric stenosis following repair of oesophageal atresia and tracheo-oesophageal fistula in a neonate

“…Foster and Shaw13 reported the association between OA and HPS for the first time in 1946. Palacios  et al 6 reported HPS in 3.3% of 61 patients they operated due to OA. van Beelen et al 4 reported HPS in 7.5% of 267 patients who underwent surgery for OA.…”