Extra-abdominal desmoid tumors

Abstract

A follow-up study of 53 patients with extra-abdominal desmoid tumor is presented. Fine-needle aspiration biopsy seemed to be valuable in the differentiation between a desmoid tumor and a truly malignant soft tissue tumor. The angiographic pictures did not differ from those of other soft tissue tumors, but valuable topographic information was obtained from the angiography in the preoperative planning. The overall local recurrence rate was 17/44, and 15 of the recurrences occurred within the first 2 years. Complete removal of the affected muscle or muscle group is recommended. Local control can be achieved by non-ablative surgery even after multiple recurrences. Only one out of 53 patients died of the tumor disease. Radiotherapy can be attempted in extensive tumors, and amputation should be reserved for tumors which have failed to respond to this treatment.

Fine-needle aspiration cytology and core needle biopsy in the preoperative diagnosis of desmoid tumors

“…CNB appears to be more reliable. ■ Desmoid tumors are rare and benign-but frequently locally aggressive-lesions originating in musculoaponeurotic tissues (Reitamo 1983, Markhede et al 1986). The tumors are often classified into 2 groups, abdominal and extra-abdominal, but the histological appearance is identical.…”

Treatment of extra-abdominal desmoid tumors with interferon-alpha with or without tretinoin

“…Most studies prove that margin status is the most important predictor of local recurrence for patients with resectable, unifocal desmoid tumors [2,8,18,[20][21][22]. About 90% of local recurrences occur within the first 2 years [9,[15][16][17].…”

“…As periods of stable disease (SD) without progression and few spontaneous regressions have been reported [13,16,17,22,35,53,64], a nonaggressive treatment was needed to achieve longer DFI or SD.…”

“…Mainly case reports and small series (<42 patients) [3,5,8,9,14,19,22,[44][45][46][47][48][49][50][51][52][53][54][55][56][57] have been reported in the literature. Larger series (45-194 patients) only appeared in conjunction with radiotherapy and/or surgery [4,[12][13][14]17,20,21,58,59].…”

Aggressive Fibromatosis in the Urological System

“…AF are categorized by their location, i.e. extra-abdominal, abdominal wall, or intra-abdominal [1][2][3] .…”