Extranodal natural killer/T-cell lymphoma, nasal type: a Spanish multicentric retrospective survey

Rozas‐Muñoz, Eduardo; Gallardo, Fernando; Pérez‐Ferriols, A.; Servitje, Octavio; Estrach, Teresa; Román, C.; Palacio-Aller, L.; Gil, Inmaculada; Martí, Rosa M.; Vidal-Sarró, David; García-Muret, M. Pilar

doi:10.1684/ejd.2017.3205

Cited by 7 publications

(1 citation statement)

References 36 publications

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“…The ENKTL was initially known as “lethal midline granuloma.” It destroys midline facial structures involving the nasal cavity, hard palate, paranasal sinuses, facial skin, oropharynx, orbits, and other organs and even in advanced stages lymph nodes ( Table 1 ) 3 4 12 13 14 15 16 . It is accompanied by obstructive symptoms, epistaxis and/or destructive mass and b symptoms (fever, night sweats and weight loss).…”

Section: Discussionmentioning

confidence: 99%

Extranodal NK/T-Cell Lymphoma, Nasal Type, Extranasal and Ulcerative Blister Variant, Case Report

Chávez Dávila,

Pinos León,

Tello Astudillo

et al. 2023

Ann Dermatol

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The extranodal natural killer (NK) T-cell lymphoma of nasal type is a form of lymphoma that falls within the WHO/EORTC 2018 classification of cutaneous T-cell lymphomas. It is characterized for being aggressive, infrequent, and destroying midline facial structures; however, it can also be in primary or secondary form at extranasal sites, such as the skin or the gastrointestinal tract, among others. We report the case of an 18-year-old patient with an extranodal NK/T-cell lymphoma located in an extranasal site. The clinical presentation is characterized for being multifocal and with erythematous-violaceous plaques that progress to hemorrhagic blisters and necrotic ulcers. Although this type of lymphoma has been reported previously by others, the presence of blisters is an atypical finding, which we believe has been described only in one case in the medical literature.

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