Favorable Outcome of Cochlear Implant in VIIIth Nerve Deficiency

Abstract

We can confirm the chance of achieving satisfactory results by CI even when the imaging of CVN is doubtful and the electrophysiological tests are disappointing. In our experience, a CI in Type IIb dysplasia of the CVN is a feasible option, provided that the candidate shows some responses at aided audiogram and at least minimal signs of language development. Adequate counseling is necessary for these children because the expected outcome is somewhat lower than that of their deaf peers with normal appearance of the nerves.

Bilateral implantation in children with cochleovestibular nerve hypoplasia

“…In most case of aplasia, poor or limited results have been reported, even though some reported cases of good results after CI in aplasia have been reported [17,18]. In those cases, the perceptive results could be due to auditory fibres contained in the facial nerve [14].…”

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“…A very thin cochlear nerve also cannot be seen on MRI and it can intermingle with facial or vestibular nerve so may be reported as cochlear agenesis. A few cochlear nerve branches could still deliver some acoustic information to the auditory center [9]. Type III: vestibular nerve is affected [10].…”

Cochlear Implantation in Patient with Cochlear Nerve Deficiency: A Case Report

“…A very thin cochlear nerve cannot seen on MRI and it can intermingled with facial or vestibular nerve so may reported as cochlear agenesis. A few cochlear nerve branches could deliver some acoustic information to the auditory center [10] .…”