Fibrosarcomatous dermatofibrosarcoma protuberans: A case report of an aggressive soft tissue sarcoma

Abstract

Dermatofibrosarcoma protuberans is a rare soft tissue neoplasm arising from mesenchymal cells, making up about 6% of all soft tissue tumours. Often found on the scalp, neck, trunk and extremities, it has an intermediate-to low-grade malignancy potential except the fibrosarcomatous variant (high-grade), which is more likely to metastasize than other types. Here we present the case of a 46-year-old male who presented with an erythematous swelling on his upper back. MRI scan suggested a mesenchymal mass, which was then excised. Histopathology was reported as fibrosarcomatous variant of dermatofibrosarcoma protuberans. He is receiving radiation at present.