Fibrosing mediastinitis and thrombosis of superior vena cava associated with Behçet's disease

Harman, Mustafa; Sayarlıoğlu, Mehmet; Arslan, Halil; Ayakta, Hayati; Harman, Ece

doi:10.1016/s0720-048x(03)00006-8

Cited by 28 publications

(16 citation statements)

References 8 publications

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“…considered an idiopathic immune-mediated reaction to different autoimmune syndromes, radiation therapy, or drugs (e.g., methysergide) [12][13][14][15][16]. Interestingly, some patients with the idiopathic form of immune-mediated FM commonly have other disease manifestations such as sclerosing cholangitis, retroperitoneal fibrosis, or…”

Section: Discussionmentioning

confidence: 99%

“…However, other infections, such as tuberculosis, aspergillosis, blastomycosis, and cryptococcosis can also cause granulomatous FM, as can sarcoidosis [7][8][9][10][11]. Nongranulomatous FM is considered an idiopathic reaction to different autoimmune syndromes, radiation therapy, Behçet disease, or treatment with methysergide [12][13][14][15][16]. Interestingly, some patients with idiopathic FM frequently have other disease manifestations such as retroperitoneal fibrosis, sclerosing cholangitis, or Riedel's thyroiditis, all of which have been associated with the IgG4-related disease (IgG4-RD) spectrum [12,[17][18][19].…”

Section: Introductionmentioning

confidence: 99%

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Idiopathic fibrosing mediastinitis: spectrum of imaging findings with emphasis on its association with IgG4-related disease

et al. 2015

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Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Idiopathic fibrosing mediastinitis: spectrum of imaging findings with emphasis on its association with IgG4-related disease

et al. 2015

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“…94 Moreover, high levels of homocysteine were reported in 64% of patients with BD with thrombosis as compared to 9% in those without thrombosis. 93 However, in a study from Tunis, 95 hyperhomocysteinemia was more frequent in patients than in controls, but there was no difference in those with or without thrombosis. Increased levels of homocysteine were also found in patients with ocular involvement compared to those with non-ocular disease and healthy control subjects.…”

Section: Homocysteinementioning

confidence: 90%

Behçet’s disease: an update on pathogenesis, diagnosis and management of vascular involvement

Kaklamanis

Calamia

2010

Rheumatol Rep

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The objective of this review is to summarize reports of the prevalence, clinical presentation, diagnostic methodology and treatment of vasculitic manifestations of Behçet’s disease (BD). We performed a literature search on vasculitis in BD. Articles were selected which provided insight into the pathogenesis and clinical aspects of vasculitis. Vasculitis underlies many of the clinical features of BD. Small vessel vasculitis is often found in the pathology of the mucocutaneous manifestations of BD. Large vessel vasculitis has been reported in 15-40% of BD patients. Ultrasound, angiography and tomography are applied to confirm the diagnosis when venous involvement is suspected. Endothelial dysfunction plays a role in the pathogenesis of disease. Peripheral arterial involvement in BD occurs in the form of arterial occlusion or aneurysms. Pulmonary arterial involvement is often life-threatening. The cause of cardiac vascular involvement requires an aggressive diagnostic approach. Corticosteroids and immunosuppressive agents have been used successfully in the early stage of large vessel disease and should be used as an adjunct to surgery. An increasing amount of data is available regarding the role of anti-tumor necrosis factor (TNF) agents for the treatment of BD. Anticoagulant therapy may be hazardous in patients with aneurysmal dilatation of the pulmonary vascular tree and is not effective in the treatment of venous thrombosis. Inflammation of small and large vessels is very frequent in BD. Both arteries and veins may be involved. Early recognition and appropriate management of large vessel vasculitis in BD is essential to reduce associated morbidity and mortality

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“…It probably constitutes a reaction to a pulmonary inflammatory process and may be paratracheal, inter-tracheo-bronchial, or interbronchial (Hiller et al 2004;Hamzaoui and Hamzaoui 2005). A fibrous mediastinitis has also been reported in association with thrombosis of the superior vena cava but it is difficult to affirm that the mediastinitis preceded the thrombosis or vice versa (Abid et al 1995;Harman et al 2003;Kanne and Mohammed 2007).…”

Section: Mediastinummentioning

confidence: 99%

Imaging Features of Behçet’s Disease

Hendaoui

Farhat

Bouhaouala

et al. 2011

Systemic Vasculitis

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Fibrosing mediastinitis and thrombosis of superior vena cava associated with Behçet's disease

Cited by 28 publications

References 8 publications

Idiopathic fibrosing mediastinitis: spectrum of imaging findings with emphasis on its association with IgG4-related disease

Idiopathic fibrosing mediastinitis: spectrum of imaging findings with emphasis on its association with IgG4-related disease

Behçet’s disease: an update on pathogenesis, diagnosis and management of vascular involvement

Imaging Features of Behçet’s Disease

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