“… 1 Epidemiologic studies suggest that the incidence of congenital SOVA ranges from 0.1% to 3.5%, with a 4:1 male predominance and incidence of rupture 5 times higher in East Asian patients than in Westerners. 2 , 3 , 4 Congenital SOVA most commonly originates from the right coronary sinus (70%-80%), followed by the noncoronary sinus (20%-30%), with <5% arising from the left coronary sinus. 5 Sakakibara and Konno subsequently classified the anatomic origin of SOVA and respective protrusion sites into 5 categories known as the Sakakibara classification, which can be simplified into the following: type I, rupture into the RV just beneath the pulmonary valve; type II, rupture into or just beneath the crista supraventricularis of the RV; type III, rupture into the RA or RV near or at the tricuspid annulus; type IV, rupture into the RA; and type V, other rare conditions, such as rupture into the LV, left atrium, pericardium, or pulmonary artery.…”