Follikuläre Mycosis fungoides (FMF)

Abstract

Follicular mycosis Fungoides (FMF) was first described in 1924. Since the first description, 22 patients with this special form of mycosis fungoides have been published. Clinical features include epidermal cysts as well as follicular papules, nodules and hyperkeratoses. FMF can be confused with acneiform dermatoses. In most cases, infiltrated plaques typical for cutaneous T cell lymphoma are also present. Histology shows a monomorphic CD4+ T cell infiltrate. Treatment and prognosis are similar of those of classical mycosis fungoides. We present one patient with FMF and review the literature of all published cases.

Follicular Mycosis Fungoides: Variability of a Rare Entity

“…6 Frequently, FMF is clinically mistaken for follicular lichen planus, lichen spinulosus, folliculitis, pityriasis rubra pilaris, acne vulgaris, or Favre-Racouchot disease. 5,7 Milia as a consequence of blistering sunburns or intense PUVA therapy are also considered differential diagnoses. Due to the low incidence of FMF, there is a lack of experience in terms of expected prognosis, clinical variability, and therapeutic response.…”