Lymphangioma occur commonly in the neck and axillae of pediatric patients, caused by an obstruction of the lymphatic flow because of congenital lymphatic malformation. However, mesenteric lmphangioma of the small intestine is a rare tumor that is seldom associated with small bowel volvulus, particularly in adult patients. Although rare, mesenteric lymphangioma can cause volvulus and intestinal obstruction by a torsion of mesentery. We report an unusual case of mesenteric lymphangioma with small bowel volvulus who was suffered from intermittent abdominal pain, treated with surgical resection.