Giant Fibromyxoid Sarcoma of the Lung: Case Report of an Extremely Rare Entity

Abstract

Low grade fibromyxoid sarcoma is a rare entity accounting fore1% of all adult cancers mostly identified in lower extremities (thigh), as well as occasional reports of sarcomas in axillae, shoulder, mediastinum, inguinal region. Primary fibromyxoid sarcoma of the lung is extremely rare phenomenon, to date, reported fewer than 10 times.

Giant primary low‐grade fibromyxoid sarcoma arising from the left pulmonary parenchyma: A case report and literature review

“…Thus, systematic investigation is necessary when labeling the tumor as primary pulmonary low‐grade fibromyxoid sarcoma to rule out metastasis. A total of five cases of primary pulmonary low‐grade fibromyxoid sarcoma have been reported previously 5–9 . In this study, we report a giant low‐grade fibromyxoid sarcoma arising from the left lung and occupying the whole left hemithorax.…”

“…A total of five cases of primary pulmonary low‐grade fibromyxoid sarcoma have been reported previously. 5 , 6 , 7 , 8 , 9 In this study, we report a giant low‐grade fibromyxoid sarcoma arising from the left lung and occupying the whole left hemithorax. The primary distinction from previous cases is the extremely large size of the tumor and the course of surgical treatment.…”

“…To the best of our knowledge, only five cases of primary pulmonary low‐grade fibromyxoid sarcoma have been reported. 5 , 6 , 7 , 8 , 9 Table 1 summarizes the characteristics of these cases. Two of these were men, and three were women.…”

“…A total of five cases of primary pulmonary low-grade fibromyxoid sarcoma have been reported previously. [5][6][7][8][9] In this study, we report a giant low-Reza Ershadi and Matin Vahedi contributed equally to this work. grade fibromyxoid sarcoma arising from the left lung and occupying the whole left hemithorax.…”

Thoracoscopic Wedge Resection for Low-Grade Fibromyxoid Sarcoma (Evans Tumor) with Massive Calcification and Originating from the Lung: A Rare Case in an Unexpected Location

“…3) LGFMS originating from the lung is extremely rare and has been previously reported in only five cases. [4][5][6][7][8] Therefore, the clinical characteristics of this tumor have not been well known and preoperative diagnosis based on clinical findings, including computed tomography (CT) scan, has been difficult. In addition, careful pathological assessment is required to correctly diagnose LGFMS, which has a benign-like histology.…”