Giant retroperitoneal desmoid tumour

Perera, ND; Vithana, V

doi:10.4038/cmj.v51i3.1262

Cited by 3 publications

(1 citation statement)

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“…Notably, extra-abdominal tumors carry a higher risk of recurrence. [13] To the best of our knowledge, only 3 cases of DTF originating from the psoas major muscle have been documented, [18][19][20] all presenting with symptoms. Among these cases, only 1 occurred in a male patient, and none exhibited hydronephrosis.…”

Section: Discussionmentioning

confidence: 99%

Incidental discovery of unilateral hydronephrosis unveiling psoas major desmoid-type fibromatosis in a 24-year-old male: A case report with a 5-year follow-up

Almjersah,

Olaisheh,

Salloum

et al. 2024

Medicine

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Rationale: Desmoid-type fibromatosis (DTF), also known as aggressive fibromatosis, is a rare neoplasm originating from the fascial or musculoaponeurotic tissues. While benign and characterized by slow growth, it exhibits local aggressiveness and lacks specific clinical characteristics. However, in a considerable percentage of patients, it could be asymptomatic and discovered by accident during routine clinical examinations. Only a few cases of DTF arising from the psoas major muscle have been reported in the medical literature. Patient concerns: A 24-year-old male, asymptomatic and without significant personal or family medical history, was diagnosed with grade 2 hydronephrosis by abdominal ultrasonography during a routine physical examination. This diagnosis was made 15 days after undergoing uncomplicated open-heart surgery to repair an atrial septal defect. Diagnosis: Intravenous pyelogram revealed hydronephrosis with dilation of the pelvicalyceal system. Ureteroscopy ruled out any intrinsic lesions of the ureter. Contrast-enhanced computed tomography identified a 3.5 × 2 × 5.2 cm mass in the retroperitoneum, closely associated with the psoas muscle and enveloping the ureter adjacent to the iliac artery. Postoperative pathological analysis confirmed a definitive diagnosis of sporadic DTF. Interventions: The patient underwent exploratory abdominal surgery, during which the tumor was resected without any intraoperative complications. Results: After close monitoring over a 5-year follow-up period, which included periodic physical examinations, magnetic resonance imaging, and ultrasonography, no local recurrence was detected. Lessons: Achieving an accurate preoperative diagnosis presents a challenge in cases involving retroperitoneal tumors originating from the psoas major muscle and encasing the ureter. However, the insertion of a double J stent is deemed a crucial step in the surgical process, facilitating the dissection and isolation of the ureter from the tumor while preserving kidney function.

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