Hemophilic Pseudotumor of the Distal Parts of the Radius and Ulna: A Case Report

Intraosseous Pseudotumor of the Distal Radius in a Patient With Hemophilia: Case Report

“…Two other reports describe children from Sudan and Turkey with pseudotumors involving the distal radius. 8,9 These other cases differ from our patient, who presented as an adult with a primary intraosseous pseudotumor in the distal radius. Given the propensity for pseudotumors to enlarge over time, we believe that it is highly unlikely that the lesion formed when our patient was a child and remained asymptomatic for almost 5 decades.…”

Pelvic Haemophilic Pseudotumour: A Case Report

“…2 It is indicated for pseudotumours located more peripherally in a welllocalised position 11 and for small peusdotumours (<3 cm in diameter). 3 In our patient, the huge pseudotumour had destroyed the ilium and sacrum. Percutaneous aspiration followed by injection of fibrin glue or bone graft is very difficult for a large pseudotumour.…”

“…9 In patients with mild haemophilia (antihaemophilic factor >5%), bleeding episodes occur less frequently after trauma or major surgery. 3,7,10 In patients with severe haemophilia (anti-haemophilic factor <1%), bleeding episodes occur more frequently and spontaneously, often after very mild trauma or daily activities. 7,10 More than 90% of bleeding episodes occur in the musculoskeletal system; of them 80% occur in joints.…”

“…Both active and passive range of movements of the hip joint were within normal range. Blood tests showed a haemoglobin level of 9.3 g/dl, haematocrit of 28%, white blood cell count of 5300/mm 3 , platelet count of 402 x10 level of 5.6% with negative anti-factor VIII. Pelvic radiographs 6 months prior to admission revealed expansile lytic lesions with ground glass appearance in the left ilium, and multiple septations accompanied by a soft-tissue mass.…”

“…15 In pseudotumour of bone, the cavity should be opened, debrided, and filled with bone grafts and bone substitute. 3 The most effective treatment for large pseudotumours is resection together with factor VIII replacement therapy. 16 In our patient, the haematoma was evacuated, the cavity was debrided and partly filled with bone grafts and bone cement, followed by reconstruction of the acetabulum with Harrington modification procedure and total hip arthroplasty.…”