Hereditary Hemorrhagic Telangiectasia: Multi–Detector Row Helical CT Assessment of Hepatic Involvement

Ianora, Amato Antonio Stabile; Memeo, M.; Sabbá, Carlo; Cirulli, Anna; Rotondò, Antonio; Angelelli, Giuseppe

doi:10.1148/radiol.2301021745

Cited by 194 publications

(160 citation statements)

References 46 publications

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“…However only 8% of such patients are symptomatic [6]. Liver involvement is characterized by diffuse vascular malformations throughout the liver that result in multiple types of shunting: hepatic artery to hepatic vein, hepatic artery to portal vein, and portal vein to hepatic vein [5,7].…”

Section: Discussionmentioning

confidence: 99%

Liver Transplantation for High Output Heart Failure Secondary to HHT: A Case Report and Review of the Literature

Martin¹,

Chinnakotla²,

Lake³

et al. 2015

J Gastrointest Dig Syst

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Section: Discussionmentioning

confidence: 99%

Liver Transplantation for High Output Heart Failure Secondary to HHT: A Case Report and Review of the Literature

Martin¹,

Chinnakotla²,

Lake³

et al. 2015

J Gastrointest Dig Syst

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“…Печеночные АВМ наблюдаются у 40-75% пациен тов с НГТ [42,43]. Однако только у 8% они бывают симптоматическими [44,45].…”

Section: клиника и диагностикаunclassified

Hereditary hemorrhagic teleangiectasia: the topical problems of diagnostics and surgical treatment

Baydarova¹,

Тупикин²,

Andreytseva³

2016

Dok. gastroenterol.

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“…HHT affects mucocutaneous tissue most frequently, but any part of the body can be affected, including the liver. The hepatic changes, including widened and tortuous hepatic arteries, telangiectases, arteriovenous and portovenous fistulas, connective tissue formation with fibrosis and atypical cirrhosis, high cardiac output, secondary congestive heart failure due to a left-to-right intrahepatic shunt, portal hypertension, gastrointestinal hemorrhage, ascites, or encephalopathy [30][31][32] . APSs are nearly universal in HHT, and HPDs often occur.…”

Section: Vascular Abnormalities and Hereditary Hemorrhagic Telangiectmentioning

confidence: 99%

Hepatic perfusion disorders: Etiopathogenesis and related diseases

Hui

Zhang²

2006

WJG

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In this article, we have reviewed the hepatic perfusion d i s o r d e r ( H P D ) , e t i o p a t h o g e n e s i s o f H P D a n d corresponding diseases. Review of the literature was based on computer searches (PubMed, Index Medicus) and personal experiences. We considered HPD reflects perfusion differences due to redistribution of arterial blood flow among segments, subsegments and lobes of the liver. The plain CT scan findings of HPD manifests as triangular or wedge-shaped areas of low attenuation. On contrast-enhanced CT scan, HPD manifests multiple (or single) transient wedge-shaped, rotundloid or irregular appearance, homogeneous hyperattenuation (in less cases, hypoattenuation) during the hepatic arterial phase (HAP) and isoattenuated or slightly hyperattenuated areas during the portal arterial phase. Dynamic enhanced magnetic resonance (MR) features are similar to enhanced CT scan. Angiographic findings include non-opacification of portal vein on portograms or wedge-shaped segmental staining in arterial and parenchymal phases on hepatic angiograms. The causes of HPD are arterioportal shunts (APS), intrahepatic vascular compressions and portal vein occlusion, steal phenomenon by hypervascular tumors, vascular variations and any other unknown reasons. It is very important for radiologists to be familiar with the various appearances of HPD to avoid false-positive diagnosis of pseudolesions and not to overestimate the extent of the disease.

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Hereditary Hemorrhagic Telangiectasia: Multi–Detector Row Helical CT Assessment of Hepatic Involvement

Abstract: Multi-detector row helical CT and reconstructions depict the complex hepatic vascular alterations typical of hereditary hemorrhagic telangiectasia.

Cited by 194 publications

References 46 publications

Liver Transplantation for High Output Heart Failure Secondary to HHT: A Case Report and Review of the Literature

Liver Transplantation for High Output Heart Failure Secondary to HHT: A Case Report and Review of the Literature

Hereditary hemorrhagic teleangiectasia: the topical problems of diagnostics and surgical treatment

Hepatic perfusion disorders: Etiopathogenesis and related diseases

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